MOLECULAR DEFECT OF SPECTRIN IN HEREDITARY PYROPOIKILOCYTOSIS - ALTERATIONS IN THE TRYPSIN-RESISTANT DOMAIN INVOLVED IN SPECTRIN SELF-ASSOCIATION

被引:81
作者
LAWLER, J
LIU, SC
PALEK, J
PRCHAL, J
机构
[1] ST ELIZABETHS HOSP,DEPT MED,BOSTON,MA 02135
[2] TUFTS UNIV,SCH MED,BOSTON,MA 02111
[3] UNIV ALABAMA,SCH MED,DEPT MED,BIRMINGHAM,AL 35294
关键词
D O I
10.1172/JCI110689
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:1019 / 1030
页数:12
相关论文
共 27 条
[1]   A MOLECULAR DEFECT IN 2 FAMILIES WITH HEMOLYTIC POIKILOCYTIC ANEMIA - REDUCTION OF HIGH-AFFINITY MEMBRANE-BINDING SITES FOR ANKYRIN [J].
AGRE, P ;
ORRINGER, EP ;
CHUI, DHK ;
BENNETT, V .
JOURNAL OF CLINICAL INVESTIGATION, 1981, 68 (06) :1566-1576
[2]  
BODMER WF, 1977, HISTOCOMPATIBILITY T
[3]   INTERACTION OF CYTOSKELETAL PROTEINS ON THE HUMAN-ERYTHROCYTE MEMBRANE [J].
BRANTON, D ;
COHEN, CM ;
TYLER, J .
CELL, 1981, 24 (01) :24-32
[4]   TRYPTIC DIGESTION OF SPECTRIN IN VARIANTS OF HEREDITARY ELLIPTOCYTOSIS [J].
COETZER, T ;
ZAIL, SS .
JOURNAL OF CLINICAL INVESTIGATION, 1981, 67 (05) :1241-1248
[5]   PREPARATION AND CHEMICAL CHARACTERISTICS OF HEMOGLOBIN-FREE GHOSTS OF HUMAN ERYTHROCYTES [J].
DODGE, JT ;
HANAHAN, DJ ;
MITCHELL, C .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1963, 100 (01) :119-&
[6]  
Fazekas de St Groth S., 1963, BIOCHIM BIOPHYS ACTA, V71, P377
[7]  
HANSPAL M, 1980, P AUST BIOCHEM SOC, V13, P12
[8]  
JI TH, 1980, J BIOL CHEM, V255, P2990
[9]   CLEAVAGE OF STRUCTURAL PROTEINS DURING ASSEMBLY OF HEAD OF BACTERIOPHAGE-T4 [J].
LAEMMLI, UK .
NATURE, 1970, 227 (5259) :680-+
[10]   SPECTRIN TETRAMER-DIMER EQUILIBRIUM AND THE STABILITY OF ERYTHROCYTE-MEMBRANE SKELETONS [J].
LIU, SC ;
PALEK, J .
NATURE, 1980, 285 (5766) :586-588