STORAGE OF MANNOSE-CONTAINING MATERIAL IN CULTURED HUMAN MANNOSIDOSIS CELLS AND METABOLIC CORRECTION BY PIG KIDNEY ALPHA-MANNOSIDASE

被引：17

作者：

MERSMANN, G ^{[1
]}

FIGURA, KV ^{[1
]}

BUDDECKE, E ^{[1
]}

机构：

[1] UNIV MUNSTER,INST PHYSIOL CHEM,D-4400 MUNSTER,FED REP GER

来源：

HOPPE-SEYLERS ZEITSCHRIFT FUR PHYSIOLOGISCHE CHEMIE | 1976年 / 357卷 / 05期

关键词：

D O I：

10.1515/bchm2.1976.357.1.641

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：641 / 648

页数：8

共 37 条

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[2] DAGLEY S, 1970, INTRO METABOLIC PATH, P137
[3] DESNICK RJ, 1973, ENZYME THERAPY GENET
[4] QUANTITATIVE ASPECTS OF PINOCYTOSIS AND INTRACELLULAR FATE OF N-ACETYL-ALPHA-D-GLUCOSAMINIDASE IN SANFILIPPO-B FIBROBLASTS
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[J]. JOURNAL OF CLINICAL INVESTIGATION, 1974, 53 (01) : 85 - 90
[5] DEFECT IN HURLER AND HUNTER SYNDROMES, .2. DEFICIENCY OF SPECIFIC FACTORS INVOLVED IN MUCOPOLYSACCHARIDE DEGRADATION
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[J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1969, 64 (01) : 360 - &
[6] DEFECT IN HURLERS AND HUNTERS SYNDROMES - FAULTY DEGRADATION OF MUCOPOLYSACCHARIDE
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[J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1968, 60 (02) : 699 - +
[7] HERS HG, 1973, LYSOSOMES STORAGE DI, P147
[8] DEFICIENCY OF ALPHA-MANNOSIDASE IN ANGUS CATTLE - INHERITED LYSOSOMAL STORAGE-DISEASE
HOCKING, JD
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JOLLY, RD
[J]. BIOCHEMICAL JOURNAL, 1972, 128 (01) : 69 - &
[9] SPECIFICITY STUDIES ON ALPHA-MANNOSIDASES USING OLIGOSACCHARIDES FROM MANNOSIDOSIS URINE AS SUBSTRATES
HULTBERG, B
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OCKERMAN, PA
[J]. BIOCHIMICA ET BIOPHYSICA ACTA, 1975, 410 (01) : 156 - 163
[10] PROPERTIES OF ALPHA-MANNOSIDASE IN MANNOSIDOSIS
HULTBERG, B
[J]. SCANDINAVIAN JOURNAL OF CLINICAL & LABORATORY INVESTIGATION, 1970, 26 (02) : 155 - &

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