TREATMENT OF HOMOZYGOUS PROTEIN-C DEFICIENCY AND NEONATAL PURPURA FULMINANS WITH A PURIFIED PROTEIN-C CONCENTRATE

被引:234
作者
DREYFUS, M
MAGNY, JF
BRIDEY, F
SCHWARZ, HP
PLANCHE, C
DEHAN, M
TCHERNIA, G
机构
[1] HOP ANTOINE BECLERE, NEONATAL INTENS CARE UNIT, F-92141 CLAMART, FRANCE
[2] HOP M LANNELONGUE, DEPT SURG, LE PLESSIS ROBINSON, FRANCE
[3] IMMUNO, VIENNA, AUSTRIA
关键词
D O I
10.1056/NEJM199111283252207
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
[No abstract available]
引用
收藏
页码:1565 / 1568
页数:4
相关论文
共 24 条
  • [1] DERMATOPATHOLOGY OF SKIN NECROSIS ASSOCIATED WITH PURPURA FULMINANS
    ADCOCK, DM
    HICKS, MJ
    [J]. SEMINARS IN THROMBOSIS AND HEMOSTASIS, 1990, 16 (04) : 283 - 292
  • [2] PROPOSED CLASSIFICATION AND PATHOLOGICAL MECHANISMS OF PURPURA FULMINANS AND SKIN NECROSIS
    ADCOCK, DM
    BROZNA, J
    MARLAR, RA
    [J]. SEMINARS IN THROMBOSIS AND HEMOSTASIS, 1990, 16 (04) : 333 - 340
  • [3] DEVELOPMENT OF THE HUMAN COAGULATION SYSTEM IN THE FULL-TERM INFANT
    ANDREW, M
    PAES, B
    MILNER, R
    JOHNSTON, M
    MITCHELL, L
    TOLLEFSEN, DM
    POWERS, P
    [J]. BLOOD, 1987, 70 (01) : 165 - 172
  • [4] PURPURA FULMINANS - A CUTANEOUS MANIFESTATION OF SEVERE PROTEIN-C DEFICIENCY
    AULETTA, MJ
    HEADINGTON, JT
    [J]. ARCHIVES OF DERMATOLOGY, 1988, 124 (09) : 1387 - 1391
  • [5] BARRETT PN, 1989, BIOTECHNOLOGIE PROTE, P399
  • [6] CAEN J, 1975, METHODES EXPLORATION
  • [7] ELSINGER F, 1986, VONWILLEBRAND FACTOR, P297
  • [8] FRIBERGER P, 1978, HAEMOSTASIS, V7, P138
  • [9] HARTMAN KR, 1989, AM J PEDIAT HEMATOL, V11, P395
  • [10] HERMSEN VM, 1990, AM J OPHTHALMOL, V109, P609