TREATMENT OF INTRACTABLE GASTROINTESTINAL MANIFESTATIONS OF CHRONIC GRANULOMATOUS-DISEASE WITH CYCLOSPORINE

被引:44
作者
ROSH, JR
TANG, HB
MAYER, L
GROISMAN, G
ABRAHAM, SK
PRINCE, A
机构
[1] COLUMBIA UNIV, COLL PHYS & SURG, DIV INFECT DIS, NEW YORK, NY 10031 USA
[2] CUNY MT SINAI SCH MED, DEPT PEDIAT, NEW YORK, NY 10029 USA
[3] CUNY MT SINAI SCH MED, DEPT MED, NEW YORK, NY 10029 USA
[4] CUNY MT SINAI SCH MED, DEPT PATHOL, NEW YORK, NY 10029 USA
关键词
D O I
10.1016/S0022-3476(95)70519-8
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Gastrointestinal manifestations of chronic granulomatous disease of childhood include granulomatous inflammatory bowel disease, Severe colitis and perirectal disease developed in a 12-year-old boy with chronic granulomatous disease while he was receiving interferon gamma therapy, The boy had a deficiency of the 22 kd light chain of the cytochrome b heterodimer. After conventional medical therapy proved to be ineffective, a rapid clinical response was obtained to cyclosporine.
引用
收藏
页码:143 / 145
页数:3
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