IMERSLUND-GRASBECK SYNDROME IN 2 BROTHERS - RENAL BIOPSY AND ULTRASTRUCTURAL FINDINGS

被引：14

作者：

LIANG, DC ^{[1
]}

HSU, HC ^{[1
]}

HUANG, FY ^{[1
]}

WEI, KN ^{[1
]}

机构：

[1] NATL TAIWAN UNIV,COLL MED,DEPT PATHOL,TAIPEI,TAIWAN

来源：

PEDIATRIC HEMATOLOGY AND ONCOLOGY | 1991年 / 8卷 / 04期

关键词：

IMERSLUND SYNDROME; MEGALOBLASTIC ANEMIA; PROTEINURIA; RENAL ULTRASTRUCTURE; VITAMIN-B12; MALABSORPTION;

D O I：

10.3109/08880019109028810

中图分类号：

R73 [肿瘤学];

学科分类号：

100214 ;

摘要：

In two Chinese siblings with Imerslund-Grasbeck syndrome, light microscopy of renal biopsies showed no remarkable change. Ultrastructurally, there were small possible focal defects in the glomerular basement membrane. Neither podocytes nor tubular cells showed evident change. No electron dense deposit was found. Our observations on renal ultrastructure differ from the previous five reports. The literature on renal pathology of this syndrome is reviewed.

引用

页码：361 / 365

页数：5

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