2 VASCULAR COMPLICATIONS OF THE EHLERS-DANLOS SYNDROME

被引：30

作者：

BREARLEY, S

FOWLER, J

HAMER, JD

机构：

[1] Department of Vascular Surgery, Queen Elizabeth Hospital, Birmingham

[2] Department of Radiology, Queen Elizabeth Hospital, Birmingham

来源：

EUROPEAN JOURNAL OF VASCULAR SURGERY | 1993年 / 7卷 / 02期

关键词：

EHLERS-DANLOS SYNDROME; VARICOSE VEINS; ARTERIAL RUPTURE; ARTERIOVENOUS FISTULA;

D O I：

10.1016/S0950-821X(05)80766-2

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Patients with Ehiers-Danlos syndrome type IV have thin walled, friable arteries and veins and are prone to spontaneous arterial rupture. We present a patient who suffered severe damage to the common femoral vein during surgery for varicose veins and who subsequently suffered a spontaneous rupture of the right external carotid artery, treated by ligation and oversewing. Intraarterial radiology and surgery in such patients are hazardous and should be avoided if possible. Where operation is essential, the simplest available procedure should be performed. Patients should be counselled to inform every doctor they consult that they have the Ehlers-Danlos syndrome. © 1993 Grune & Stratton Ltd.

引用

页码：210 / 213

页数：4

共 15 条

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