THE SYNTHESIS AND CHARACTERIZATION OF 2-METHYLACETOACETYL COENZYME-A AND ITS USE IN THE IDENTIFICATION OF THE SITE OF THE DEFECT IN 2-METHYLACETOACETIC AND 2-METHYL-3-HYDROXYBUTYRIC ACIDURIA
被引:75
作者:
MIDDLETON, B
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机构:UNIV NEWCASTLE UPON TYNE,ROYAL VICTORIA INFIRM,DEPT CLIN BIOCHEM & METAB MED,NEWCASTLE TYNE NE1 4LP,TYNE & WEAR,ENGLAND
MIDDLETON, B
BARTLETT, K
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h-index: 0
机构:UNIV NEWCASTLE UPON TYNE,ROYAL VICTORIA INFIRM,DEPT CLIN BIOCHEM & METAB MED,NEWCASTLE TYNE NE1 4LP,TYNE & WEAR,ENGLAND
BARTLETT, K
机构:
[1] UNIV NEWCASTLE UPON TYNE,ROYAL VICTORIA INFIRM,DEPT CLIN BIOCHEM & METAB MED,NEWCASTLE TYNE NE1 4LP,TYNE & WEAR,ENGLAND