THE SYNTHESIS AND CHARACTERIZATION OF 2-METHYLACETOACETYL COENZYME-A AND ITS USE IN THE IDENTIFICATION OF THE SITE OF THE DEFECT IN 2-METHYLACETOACETIC AND 2-METHYL-3-HYDROXYBUTYRIC ACIDURIA

被引:75
作者
MIDDLETON, B
BARTLETT, K
机构
[1] UNIV NEWCASTLE UPON TYNE,ROYAL VICTORIA INFIRM,DEPT CLIN BIOCHEM & METAB MED,NEWCASTLE TYNE NE1 4LP,TYNE & WEAR,ENGLAND
[2] UNIV NOTTINGHAM,SCH MED,DEPT BIOCHEM,NOTTINGHAM NG7 2RD,ENGLAND
关键词
D O I
10.1016/0009-8981(83)90329-7
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
摘要
引用
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页码:291 / 305
页数:15
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