URINARY SEDIMENT DOLICHOL EXCRETION IN PATIENTS WITH BATTEN DISEASE AND OTHER NEURODEGENERATIVE AND STORAGE DISORDERS

被引:24
作者
BENNETT, MJ
MATHERS, NJ
HEMMING, FW
ZWEIJEHOFMAN, I
HOSKING, GP
机构
[1] SHEFFIELD CHILDRENS HOSP,RYEGATE CTR,SHEFFIELD S10 2TH,ENGLAND
[2] UNIV NOTTINGHAM,SCH MED,DEPT BIOCHEM,NOTTINGHAM NG7 2YH,ENGLAND
[3] BARTIMEUSHAGE,DOORN,NETHERLANDS
关键词
D O I
10.1203/00006450-198502000-00014
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:213 / 216
页数:4
相关论文
共 19 条
  • [1] ULTRASTRUCTURAL CHARACTERISTICS OF ABNORMAL CYTOSOMES IN BATTEN-KUFS DISEASE
    CARPENTER, S
    KARPATI, G
    ANDERMANN, F
    JACOB, JC
    ANDERMANN, E
    [J]. BRAIN, 1977, 100 (MAR) : 137 - 156
  • [2] de Baecque C M, 1976, Arch Pathol Lab Med, V100, P139
  • [3] DEBAECQUE C, 1975, NEW ENGL J MED, V292, P1408
  • [4] CONTROL AND MANIPULATION OF THE PHOSPHODOLICHOL PATHWAY OF PROTEIN N-GLYCOSYLATION
    HEMMING, FW
    [J]. BIOSCIENCE REPORTS, 1982, 2 (04) : 203 - 221
  • [5] KIN NMKNY, 1982, PEDIATR RES, V16, P530
  • [6] HIGH-LEVELS OF BRAIN DOLICHOLS IN NEURONAL CEROID-LIPOFUSCINOSIS AND SENESCENCE
    KIN, NMKNY
    PALO, J
    HALTIA, M
    WOLFE, LS
    [J]. JOURNAL OF NEUROCHEMISTRY, 1983, 40 (05) : 1465 - 1473
  • [7] LAKE BD, 1981, PEDIATR PATHOL, P617
  • [8] PULLARKAT RK, 1982, J BIOL CHEM, V257, P5991
  • [9] OCCURRENCE OF DOLICHOL IN HUMAN TISSUES
    RUPAR, CA
    CARROLL, KK
    [J]. LIPIDS, 1978, 13 (04) : 291 - 293
  • [10] SCHUURMANSSTEKH.JH, 1977, ACTA NEUROPATHOL BER, V38, P137