AGGRESSIVE RESPIRATORY SUPPORT AND UNILATERAL NEPHRECTOMY FOR INFANTS WITH SEVERE PERINATAL AUTOSOMAL RECESSIVE POLYCYSTIC KIDNEY-DISEASE

被引：17

作者：

BEAN, SA

BEDNAREK, FJ

PRIMACK, WA

机构：

[1] MED CTR CENT MASSACHUSETTS, DIV NEONATOL, WORCESTER, MA USA

[2] FALLON CLIN INC, DEPT PEDIAT, WORCESTER, MA USA

[3] UNIV MASSACHUSETTS, MED CTR, DEPT PEDIAT, WORCESTER, MA 01605 USA

来源：

JOURNAL OF PEDIATRICS | 1995年 / 127卷 / 02期

关键词：

D O I：

10.1016/S0022-3476(95)70318-7

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Newborn infants with severe autosomal recessive polycystic kidney disease often receive minimal intervention because poor respiratory and renal outcomes are anticipated. We describe two patients whose respiratory failure was successfully treated with aggressive intervention. Massive kidneys restricted gastrointestinal capacity and limited feedings. Uninephrectomy allowed adequate enteral feedings and preserved sufficient renal function for homeostasis and growth.

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收藏

页码：311 / 313

页数：3

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