BIOLOGY OF NEURONAL DYSFUNCTION IN STORAGE DISORDERS

被引:17
作者
WALKLEY, SU
MARCH, PA
机构
[1] Department of Neuroscience, Rose F. Kennedy Center for Research in Mental Retardation and Human Development, Albert Einstein College of Medicine, Bronx, 10461, NY
关键词
D O I
10.1007/BF00710266
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
[No abstract available]
引用
收藏
页码:284 / 287
页数:4
相关论文
共 12 条
[1]   PIGMENTOARCHITECTONIC PATHOLOGY OF THE ISOCORTEX IN JUVENILE NEURONAL CEROID-LIPOFUSCINOSIS - AXONAL ENLARGEMENTS IN LAYER-IIIAB AND CELL LOSS IN LAYER-V [J].
BRAAK, H ;
GOEBEL, HH .
ACTA NEUROPATHOLOGICA, 1979, 46 (1-2) :79-83
[2]   ECTOPIC DENDRITES OCCUR ONLY ON CORTICAL PYRAMIDAL CELLS CONTAINING ELEVATED GM2 GANGLIOSIDE IN ALPHA-MANNOSIDOSIS [J].
GOODMAN, LA ;
LIVINGSTON, PO ;
WALKLEY, SU .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1991, 88 (24) :11330-11334
[3]   STUDIES OF UPTAKE OF H-3-GABA AND [H-3]GLYCINE IN SLICES AND HOMOGENATES OF RAT-BRAIN AND SPINAL-CORD BY ELECTRON-MICROSCOPIC AUTORADIOGRAPHY [J].
IVERSEN, LL ;
BLOOM, FE .
BRAIN RESEARCH, 1972, 41 (01) :131-&
[4]  
PALMER DN, 1990, LIPOFUSCIN CEROID PI, P211
[5]   METABOLISM AND NERVOUS-SYSTEM DISEASE - A CHALLENGE FOR OUR TIMES .2. [J].
ROBERTS, E .
METABOLIC BRAIN DISEASE, 1986, 1 (02) :91-117
[6]   CHANGES IN GANGLIOSIDE COMPOSITION IN INHERITED AND SWAINSONINE-INDUCED ALPHA-MANNOSIDOSIS [J].
SIEGEL, DA ;
WALKLEY, SU .
JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY, 1989, 48 (03) :350-350
[7]  
SIEGEL DA, 1990, T AM SOC NEUROCHEM, V21, P110
[8]  
WALKLEY S U, 1989, Society for Neuroscience Abstracts, V15, P937
[9]  
WALKLEY SU, 1988, J NEUROSCI, V8, P445
[10]   NEUROAXONAL DYSTROPHY IN NEURONAL STORAGE DISORDERS - EVIDENCE FOR MAJOR GABAERGIC NEURON INVOLVEMENT [J].
WALKLEY, SU ;
BAKER, HJ ;
RATTAZZI, MC ;
HASKINS, ME ;
WU, JY .
JOURNAL OF THE NEUROLOGICAL SCIENCES, 1991, 104 (01) :1-8