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SERUM VERY LONG-CHAIN FATTY-ACID PATTERN IN ZELLWEGER SYNDROME
被引:46
作者
:
BAKKEREN, JAJM
论文数:
0
引用数:
0
h-index:
0
BAKKEREN, JAJM
MONNENS, LAH
论文数:
0
引用数:
0
h-index:
0
MONNENS, LAH
TRIJBELS, JMF
论文数:
0
引用数:
0
h-index:
0
TRIJBELS, JMF
MAAS, JM
论文数:
0
引用数:
0
h-index:
0
MAAS, JM
机构
:
来源
:
CLINICA CHIMICA ACTA
|
1984年
/ 138卷
/ 03期
关键词
:
D O I
:
10.1016/0009-8981(84)90140-2
中图分类号
:
R446 [实验室诊断];
R-33 [实验医学、医学实验];
学科分类号
:
1001 ;
摘要
:
引用
收藏
页码:325 / 331
页数:7
相关论文
共 22 条
[1]
BROWN FR, 1982, JOHNS HOPKINS MED J, V151, P344
[2]
BROWN FR, 1982, JOHNS HOPKINS MED J, V151, P164
[3]
FOLCH J, 1957, J BIOL CHEM, V226, P497
[4]
PEROXISOMAL AND MITOCHONDRIAL DEFECTS IN CEREBRO-HEPATO-RENAL SYNDROME
GOLDFISCHER, S
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
GOLDFISCHER, S
MOORE, CL
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
MOORE, CL
JOHNSON, AB
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
JOHNSON, AB
SPIRO, AJ
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
SPIRO, AJ
VALSAMIS, MP
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
VALSAMIS, MP
WISNIEWSKI, HK
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
WISNIEWSKI, HK
RITCH, RH
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
RITCH, RH
NORTON, WT
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
NORTON, WT
RAPIN, I
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
RAPIN, I
GARTNER, LM
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
GARTNER, LM
[J].
SCIENCE,
1973,
182
(4107)
: 62
-
64
[5]
CEREBRO-HEPATO-RENAL SYNDROME OF ZELLWEGER - CLINICAL SYMPTOMS AND RELEVANT LABORATORY FINDINGS IN 16 PATIENTS
GOVAERTS, L
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
GOVAERTS, L
MONNENS, L
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
MONNENS, L
TEGELAERS, W
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
TEGELAERS, W
TRIJBELS, F
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
TRIJBELS, F
VANRAAYSELTEN, A
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
VANRAAYSELTEN, A
[J].
EUROPEAN JOURNAL OF PEDIATRICS,
1982,
139
(02)
: 125
-
128
[6]
SEVERE PLASMALOGEN DEFICIENCY IN TISSUES OF INFANTS WITHOUT PEROXISOMES (ZELLWEGER SYNDROME)
HEYMANS, HSA
论文数:
0
引用数:
0
h-index:
0
机构:
STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
HEYMANS, HSA
SCHUTGENS, RBH
论文数:
0
引用数:
0
h-index:
0
机构:
STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
SCHUTGENS, RBH
TAN, R
论文数:
0
引用数:
0
h-index:
0
机构:
STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
TAN, R
VANDENBOSCH, H
论文数:
0
引用数:
0
h-index:
0
机构:
STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
VANDENBOSCH, H
BORST, P
论文数:
0
引用数:
0
h-index:
0
机构:
STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
BORST, P
[J].
NATURE,
1983,
306
(5938)
: 69
-
70
[7]
CHAIN-LENGTH SPECIFICITIES OF PEROXISOMAL AND MITOCHONDRIAL BETA-OXIDATION IN RAT-LIVER
HRYB, DJ
论文数:
0
引用数:
0
h-index:
0
机构:
CUNY QUEENS COLL, DEPT CHEM, FLUSHING, NY 11367 USA
CUNY QUEENS COLL, DEPT CHEM, FLUSHING, NY 11367 USA
HRYB, DJ
HOGG, JF
论文数:
0
引用数:
0
h-index:
0
机构:
CUNY QUEENS COLL, DEPT CHEM, FLUSHING, NY 11367 USA
CUNY QUEENS COLL, DEPT CHEM, FLUSHING, NY 11367 USA
HOGG, JF
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1979,
87
(04)
: 1200
-
1206
[8]
VERY LONG-CHAIN FATTY-ACID OXIDATION IN RAT-LIVER
KAWAMURA, N
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV,SCH MED,DEPT NEUROL,BALTIMORE,MD 21205
JOHNS HOPKINS UNIV,SCH MED,DEPT NEUROL,BALTIMORE,MD 21205
KAWAMURA, N
MOSER, HW
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV,SCH MED,DEPT NEUROL,BALTIMORE,MD 21205
JOHNS HOPKINS UNIV,SCH MED,DEPT NEUROL,BALTIMORE,MD 21205
MOSER, HW
KISHIMOTO, Y
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV,SCH MED,DEPT NEUROL,BALTIMORE,MD 21205
JOHNS HOPKINS UNIV,SCH MED,DEPT NEUROL,BALTIMORE,MD 21205
KISHIMOTO, Y
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1981,
99
(04)
: 1216
-
1225
[9]
FATTY ACYL-COA OXIDIZING SYSTEM IN RAT-LIVER PEROXISOMES - ENHANCEMENT BY CLOFIBRATE, A HYPOLIPIDEMIC DRUG
LAZAROW, PB
论文数:
0
引用数:
0
h-index:
0
机构:
ROCKEFELLER UNIV,NEW YORK,NY 10021
ROCKEFELLER UNIV,NEW YORK,NY 10021
LAZAROW, PB
DEDUVE, C
论文数:
0
引用数:
0
h-index:
0
机构:
ROCKEFELLER UNIV,NEW YORK,NY 10021
ROCKEFELLER UNIV,NEW YORK,NY 10021
DEDUVE, C
[J].
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA,
1976,
73
(06)
: 2043
-
2046
[10]
MANNAERTS GP, 1979, J BIOL CHEM, V254, P4585
←
1
2
3
→
共 22 条
[1]
BROWN FR, 1982, JOHNS HOPKINS MED J, V151, P344
[2]
BROWN FR, 1982, JOHNS HOPKINS MED J, V151, P164
[3]
FOLCH J, 1957, J BIOL CHEM, V226, P497
[4]
PEROXISOMAL AND MITOCHONDRIAL DEFECTS IN CEREBRO-HEPATO-RENAL SYNDROME
GOLDFISCHER, S
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
GOLDFISCHER, S
MOORE, CL
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
MOORE, CL
JOHNSON, AB
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
JOHNSON, AB
SPIRO, AJ
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
SPIRO, AJ
VALSAMIS, MP
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
VALSAMIS, MP
WISNIEWSKI, HK
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
WISNIEWSKI, HK
RITCH, RH
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
RITCH, RH
NORTON, WT
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
NORTON, WT
RAPIN, I
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
RAPIN, I
GARTNER, LM
论文数:
0
引用数:
0
h-index:
0
机构:
ALBERT EINSTEIN COLL MED, ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN, BRONX, NY 10461 USA
GARTNER, LM
[J].
SCIENCE,
1973,
182
(4107)
: 62
-
64
[5]
CEREBRO-HEPATO-RENAL SYNDROME OF ZELLWEGER - CLINICAL SYMPTOMS AND RELEVANT LABORATORY FINDINGS IN 16 PATIENTS
GOVAERTS, L
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
GOVAERTS, L
MONNENS, L
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
MONNENS, L
TEGELAERS, W
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
TEGELAERS, W
TRIJBELS, F
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
TRIJBELS, F
VANRAAYSELTEN, A
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
UNIV AMSTERDAM,ACADEM MED CTR,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
VANRAAYSELTEN, A
[J].
EUROPEAN JOURNAL OF PEDIATRICS,
1982,
139
(02)
: 125
-
128
[6]
SEVERE PLASMALOGEN DEFICIENCY IN TISSUES OF INFANTS WITHOUT PEROXISOMES (ZELLWEGER SYNDROME)
HEYMANS, HSA
论文数:
0
引用数:
0
h-index:
0
机构:
STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
HEYMANS, HSA
SCHUTGENS, RBH
论文数:
0
引用数:
0
h-index:
0
机构:
STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
SCHUTGENS, RBH
TAN, R
论文数:
0
引用数:
0
h-index:
0
机构:
STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
TAN, R
VANDENBOSCH, H
论文数:
0
引用数:
0
h-index:
0
机构:
STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
VANDENBOSCH, H
BORST, P
论文数:
0
引用数:
0
h-index:
0
机构:
STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
BORST, P
[J].
NATURE,
1983,
306
(5938)
: 69
-
70
[7]
CHAIN-LENGTH SPECIFICITIES OF PEROXISOMAL AND MITOCHONDRIAL BETA-OXIDATION IN RAT-LIVER
HRYB, DJ
论文数:
0
引用数:
0
h-index:
0
机构:
CUNY QUEENS COLL, DEPT CHEM, FLUSHING, NY 11367 USA
CUNY QUEENS COLL, DEPT CHEM, FLUSHING, NY 11367 USA
HRYB, DJ
HOGG, JF
论文数:
0
引用数:
0
h-index:
0
机构:
CUNY QUEENS COLL, DEPT CHEM, FLUSHING, NY 11367 USA
CUNY QUEENS COLL, DEPT CHEM, FLUSHING, NY 11367 USA
HOGG, JF
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1979,
87
(04)
: 1200
-
1206
[8]
VERY LONG-CHAIN FATTY-ACID OXIDATION IN RAT-LIVER
KAWAMURA, N
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV,SCH MED,DEPT NEUROL,BALTIMORE,MD 21205
JOHNS HOPKINS UNIV,SCH MED,DEPT NEUROL,BALTIMORE,MD 21205
KAWAMURA, N
MOSER, HW
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV,SCH MED,DEPT NEUROL,BALTIMORE,MD 21205
JOHNS HOPKINS UNIV,SCH MED,DEPT NEUROL,BALTIMORE,MD 21205
MOSER, HW
KISHIMOTO, Y
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV,SCH MED,DEPT NEUROL,BALTIMORE,MD 21205
JOHNS HOPKINS UNIV,SCH MED,DEPT NEUROL,BALTIMORE,MD 21205
KISHIMOTO, Y
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1981,
99
(04)
: 1216
-
1225
[9]
FATTY ACYL-COA OXIDIZING SYSTEM IN RAT-LIVER PEROXISOMES - ENHANCEMENT BY CLOFIBRATE, A HYPOLIPIDEMIC DRUG
LAZAROW, PB
论文数:
0
引用数:
0
h-index:
0
机构:
ROCKEFELLER UNIV,NEW YORK,NY 10021
ROCKEFELLER UNIV,NEW YORK,NY 10021
LAZAROW, PB
DEDUVE, C
论文数:
0
引用数:
0
h-index:
0
机构:
ROCKEFELLER UNIV,NEW YORK,NY 10021
ROCKEFELLER UNIV,NEW YORK,NY 10021
DEDUVE, C
[J].
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA,
1976,
73
(06)
: 2043
-
2046
[10]
MANNAERTS GP, 1979, J BIOL CHEM, V254, P4585
←
1
2
3
→