IMMUNOLOGICAL EVIDENCE FOR AN ORNITHINE TRANSCARBAMYLASE LESION RESULTING IN THE FORMATION OF ENZYME WITH SMALLER PROTEIN SUBUNITS

被引:7
作者
HOOGENRAAD, N [1 ]
DEMARTINIS, ML [1 ]
DANKS, DM [1 ]
机构
[1] ROYAL CHILDRENS HOSP, BIRTH DEFECTS RES INST, PARKVILLE, VIC 3052, AUSTRALIA
关键词
D O I
10.1007/BF02310869
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:149 / 152
页数:4
相关论文
共 19 条
[1]   ELECTROPHORETIC TRANSFER OF PROTEINS AND NUCLEIC-ACIDS FROM SLAB GELS TO DIAZOBENZYLOXYMETHYL CELLULOSE OR NITROCELLULOSE SHEETS [J].
BITTNER, M ;
KUPFERER, P ;
MORRIS, CF .
ANALYTICAL BIOCHEMISTRY, 1980, 102 (02) :459-471
[2]   HEMOGLOBIN GUN HILL - DELETION OF 5 AMINO ACID RESIDUES AND IMPAIRED HEME-GLOBIN BINDING [J].
BRADLEY, TB ;
WOHL, RC ;
RIEDER, RF .
SCIENCE, 1967, 157 (3796) :1581-&
[3]   ORNITHINE TRANSCARBAMYLASE DEFICIENCIES IN HUMAN MALES KINETIC AND IMMUNOCHEMICAL CLASSIFICATION [J].
BRIAND, P ;
FRANCOIS, B ;
RABIER, D ;
CATHELINEAU, L .
BIOCHIMICA ET BIOPHYSICA ACTA, 1982, 704 (01) :100-106
[4]  
BRIAND P, 1981, FEBS LETT, V130, P65, DOI 10.1016/0014-5793(81)80666-7
[5]  
BURNETTE WN, 1981, ANAL BIOCHEM, V112, P195, DOI 10.1016/0003-2697(81)90281-5
[6]   INVITRO SYNTHESIS OF A PUTATIVE PRECURSOR OF MITOCHONDRIAL ORNITHINE TRANSCARBAMOYLASE [J].
CONBOY, JG ;
KALOUSEK, F ;
ROSENBERG, LE .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1979, 76 (11) :5724-5727
[7]  
DEMARTINIS ML, 1981, BIOCHEM INT, V3, P371
[8]  
HAAN EA, 1979, AUST PAEDIATR J, V15, P142
[9]   PURIFICATION OF ORNITHINE TRANSCARBAMYLASE FROM RAT-LIVER BY AFFINITY-CHROMATOGRAPHY WITH IMMOBILIZED TRANSITION-STATE ANALOG [J].
HOOGENRAAD, NJ ;
SUTHERLAND, TM ;
HOWLETT, GJ .
ANALYTICAL BIOCHEMISTRY, 1980, 101 (01) :97-102
[10]  
HSIA YE, 1974, GASTROENTEROLOGY, V67, P347