INCORPORATION OF [C-14] GLUCOSE INTO ALPHA-1,4 BONDS OF GLYCOGEN BY LEUKOCYTES AND FIBROBLASTS OF PATIENTS WITH TYPE-III GLYCOGEN-STORAGE DISEASE

被引：10

作者：

GUTMAN, A

BARASH, V

SCHRAMM, H

DECKELBAUM, RJ

GRANOT, E

AKER, M

KOHN, G

机构：

[1] HADASSAH UNIV HOSP,DEPT CLIN BIOCHEM,IL-91120 JERUSALEM,ISRAEL

[2] HADASSAH UNIV HOSP,DEPT CLIN GENET,IL-91120 JERUSALEM,ISRAEL

[3] HADASSAH UNIV HOSP,DEPT PEDIAT,IL-91120 JERUSALEM,ISRAEL

来源：

PEDIATRIC RESEARCH | 1985年 / 19卷 / 01期

关键词：

D O I：

10.1203/00006450-198501000-00009

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

引用

页码：28 / 32

页数：5

共 24 条

[1] REGULATION OF GLYCOGEN-SYNTHETASE AND PHOSPHORYLASE PHOSPHATASE-ACTIVITIES IN RAT ADIPOSE-TISSUE [J].

BARASH, V ;

SCHRAMM, H ;

GUTMAN, A .

BIOCHIMICA ET BIOPHYSICA ACTA, 1977, 481 (01) :86-95

[2] DEBRANCHING ENZYME FROM RABBIT SKELETAL-MUSCLE - EVIDENCE FOR LOCATION OF 2 ACTIVE-CENTERS ON A SINGLE POLYPEPTIDE-CHAIN [J].

BATES, EJ ;

HEATON, GM ;

TAYLOR, C ;

KERNOHAN, JC ;

COHEN, P .

FEBS LETTERS, 1975, 58 (01) :181-185

[3] TYPE 3 GLYCOGENOSIS - A FAMILY WITH AN UNUSUAL TISSUE DISTRIBUTION OF ENZYME LESION [J].

BRANDT, IK ;

DELUCA, VA .

AMERICAN JOURNAL OF MEDICINE, 1966, 40 (05) :779-+

[4]

BROWN DH, 1978, J BIOL CHEM, V253, P5005

[5] PROPERTIES OF AN OLIGO-1,4-] 1,4-GLUCANTRANSFERASE FROM ANIMAL TISSUES [J].

BROWN, DH ;

ILLINGWORTH, B .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1962, 48 (10) :1783-&

[6] STRUCTURE OF POLYSACCHARIDE FORMED BY INCUBATING GLYCOGEN WITH D-GLUCOSE-C-14 IN PRESENCE OF GLYCOGEN DEBRANCHING ENZYME [AMYLO-(1 -] 6)-GLUCOSIDASE-4-ALPHA-GLUCANOTRANSFERASE] [J].

BROWN, DH ;

SPRINKLE, DJ ;

BROWN, BI .

CARBOHYDRATE RESEARCH, 1978, 61 (MAR) :265-277

[7] TYPE-III GLYCOGENOSIS - ATYPICAL ENZYME-ACTIVITIES IN BLOOD-CELLS IN 2 SIBLINGS [J].

DECKELBAUM, RJ ;

AGAM, G ;

RUSSELL, A ;

SHAPIRA, E ;

COHEN, T ;

GUTMAN, A .

JOURNAL OF PEDIATRICS, 1972, 81 (05) :955-+

[8] GLYCOGEN METABOLISM OF HUMAN DIPLOID FIBROBLAST CELLS IN CULTURE .1. STUDIES OF CELLS FROM PATIENTS WITH GLYCOGENOSIS TYPES-II, III, AND V [J].

DIMAURO, S ;

ROWLAND, LP ;

MELLMAN, WJ .

PEDIATRIC RESEARCH, 1973, 7 (09) :739-744

[9]

HERS H G, 1959, Rev Int Hepatol, V9, P35

[10] DETERMINATION OF AMYLO-1,6-GLUCOSIDASE [J].

HERS, HG ;

VERHUE, W ;

VANHOOF, F .

EUROPEAN JOURNAL OF BIOCHEMISTRY, 1967, 2 (03) :257-+

← 1 2 3 →