SKELETAL-MUSCLE NAD+(P) AND NADP+-DEPENDENT MALIC ENZYME IN FRIEDREICHS ATAXIA

被引:19
作者
BOTTACCHI, E [1 ]
DIDONATO, S [1 ]
机构
[1] IST NEUROL C BESTA,NEUROMETAB DIS LAB,VIA CELORIA 11,I-20133 MILAN,ITALY
关键词
D O I
10.1212/WNL.33.6.712
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:712 / 716
页数:5
相关论文
共 18 条
[1]   EFFECT OF GENE DOSAGE ON EXPRESSION OF MITOCHONDRIAL MALIC ENZYME-ACTIVITY IN MOUSE [J].
BERNSTINE, EG ;
RUSSELL, LB ;
CAIN, CS .
NATURE, 1978, 271 (5647) :748-750
[2]  
CATE RL, 1979, J BIOL CHEM, V254, P1659
[3]  
CZOK R, 1974, VERLAG CHEM, V4, P1836
[4]  
DANGELO A, 1980, ITAL J NEUROL SCI, V4, P231
[5]  
HSU RY, 1967, J BIOL CHEM, V242, P520
[6]   PYRUVATE-DEHYDROGENASE DEFICIENCY IN SPINOCEREBELLAR DEGENERATIONS [J].
KARK, RAP ;
RODRIGUEZBUDELLI, M .
NEUROLOGY, 1979, 29 (01) :126-131
[7]  
LEITER AB, 1978, J BIOL CHEM, V253, P2716
[8]  
LIN RC, 1974, J BIOL CHEM, V249, P3867
[9]   BIOCHEMICAL STUDIES OF SKELETAL MUSCLE MITOCHONDRIA .I. MICROANALYSIS OF CYTOCHROME CONTENT OXIDATIVE AND PHOSPHORYLATIVE ACTIVITIES OF MAMMALIAN SKELETAL MUSCLE MITOCHONDRIA [J].
MAKINEN, MW ;
LEE, CP .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1968, 126 (01) :75-&
[10]  
MANDELLA RD, 1975, J BIOL CHEM, V250, P5877