INTRACISTERNAL COLLAGEN FIBRILS IN PROLIFERATIVE FASCIITIS AND MYOSITIS OF CHILDHOOD

被引:11
作者
GHADIALLY, FN [1 ]
THOMAS, J [1 ]
JABI, M [1 ]
RIPPSTEIN, P [1 ]
机构
[1] OTTAWA CIVIC HOSP,DEPT PATHOL,OTTAWA K1Y 4M9,ON,CANADA
关键词
DIAGNOSTIC VALUE OF INTRACELLULAR COLLAGEN; INTRACISTERNAL COLLAGEN; MYOSITIS; PROLIFERATIVE FASCIITIS; SHORT SPACING COLLAGEN FIBRILS;
D O I
10.3109/01913129309084036
中图分类号
TH742 [显微镜];
学科分类号
摘要
During ultrastructural examination of a difficult to diagnose tumor, short spacing collagen fibrils (periodicity of banding, approximately 43.2 nm) and native collagen fibrils (periodicity of banding, approximately 53 nm) were found in dilated and vacuolated cisternae of rough endoplasmic reticulum and the perinuclear cistern. Original diagnoses from several histopathologists included alveolar soft part sarcoma, malignant fibrous histiocytoma, atypical fibroxanthoma, and myogenic tumor. The finding of intracisternal collagen (which is but a variety of intracellular collagen) led to the conclusion that this was a fibroblastic neoplasm. This, plus a review of the histologic findings, led to the diagnosis of proliferative fasciitis and myositis of childhood.
引用
收藏
页码:161 / 168
页数:8
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