ASYMPTOMATIC LARGE HYPOTHALAMIC HAMARTOMA ASSOCIATED WITH POLYDACTYLY IN AN ADULT

被引:13
作者
CHENG, K [1 ]
SAWAMURA, Y [1 ]
YAMAUCHI, T [1 ]
ABE, H [1 ]
LEIBROCK, LG [1 ]
RICCARDI, VM [1 ]
机构
[1] HOKKAIDO UNIV,SCH MED,DEPT NEUROSURG,NORTH 15,W 7,KITA KU,SAPPORO,HOKKAIDO 060,JAPAN
关键词
HAMARTOMA; HYPOTHALAMUS; MAGNETIC RESONANCE IMAGING; POLYDACTYLY;
D O I
10.1227/00006123-199303000-00020
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A HYPOTHALAMIC HAMARTOMA is a congenital tumor-like neural malformation. It is usually seen in children and is associated with neuroendocrinological symptoms, seizures, or psychological impairments. An asymptomatic hypothalamic hamartoma in an adult is extremely rare. This report describes an asymptomatic adult with a large hypothalamic hamartoma associated with polydactyly in his feet. Both polydactyly and hamartoma are rare lesions; therefore, this may not be a coincidental presentation. It is thought to have occurred in the embryonic period presumably between 37 and 40 gestational days.
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页码:458 / 460
页数:3
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