FAMILIAL DEMENTIA WITH PICKS CELLS - A CASE-REPORT OF PROBABLE FAMILIAL PICKS-DISEASE

被引:8
作者
GAUGHRAN, F
KEOHANE, C
BUCKLEY, M
机构
[1] CORK REG HOSP, DEPT PATHOL, NEUROPATHOL LAB, CORK, IRELAND
[2] ST STEPHENS HOSP, DEPT PSYCHIAT, GLANMIRE, CORK, IRELAND
关键词
ATYPICAL PICKS DISEASE; FAMILIAL DEMENTIA; PICKS CELLS;
D O I
10.1017/S0790966700016049
中图分类号
R749 [精神病学];
学科分类号
100205 ;
摘要
The clinical and pathological features are described in a case of prolonged dementia in a 59 year old man with familial dementia and extrapyramidal disorder. Postmortem examination showed severe fronto-temporal and basal ganglia atrophy, with many ''ballooned neurons'' in the residual cortex most likely representing Pick's disease. The differential diagnosis is discussed and aspects of this rare condition are reviewed.
引用
收藏
页码:34 / 38
页数:5
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