THE CLINICOPATHOLOGICAL FEATURES OF FAMILIAL CYLINDROMAS AND TRICHOEPITHELIOMAS (BROOKE-SPIEGLER SYNDROME) - A REPORT OF 2 FAMILIES

被引:27
作者
BURROWS, NP [1 ]
JONES, RR [1 ]
SMITH, NP [1 ]
机构
[1] ST THOMAS HOSP,LONDON SE1 7EH,ENGLAND
关键词
D O I
10.1111/j.1365-2230.1992.tb00223.x
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
We have studied four patients from two families and obtained the clinical data from four other affected family members who demonstrated the coexistence of multiple cylindromas and trichoepitheliomas. An autosomal dominant pattern of inheritance with variable penetrance was exhibited in both families, with a female to male ratio of 3:1. The clinical and pathological features of this rare association are discussed.
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页码:332 / 336
页数:5
相关论文
共 25 条
[1]  
Adamson HG, 1914, LANCET, V1, P810
[2]  
Ancell H, 1842, Med Chir Trans, V25, P227
[3]  
BROOKE HG, 1982, BRIT J DERMATOL, V4, P296
[4]  
CHALSTREY LJ, 1955, ST BARTS HOSP J, V59, P378
[5]   DERMAL CYLINDROMAS ORIGINATE FROM THE ECCRINE SWEAT GLAND [J].
COTTON, DWK ;
BRAYE, SG .
BRITISH JOURNAL OF DERMATOLOGY, 1984, 111 (01) :53-61
[6]  
CRAIN RC, 1961, AM J CLIN PATHOL, V35, P504
[7]   HEREDITARY MULTIPLE BENIGN CYSTIC EPITHELIOMA [J].
FLIEGELMAN, MT ;
KRUSE, WT .
JOURNAL OF INVESTIGATIVE DERMATOLOGY, 1948, 11 (03) :189-196
[8]  
FUSARO RM, 1962, J INVEST DERMATOL, V3, P137
[9]   HEREDITY OF MULTIPLE BENIGN CYSTIC EPITHELIOMA - THE INDIANA FAMILY [J].
GAUL, LE .
AMA ARCHIVES OF DERMATOLOGY AND SYPHILOLOGY, 1953, 68 (05) :517-524
[10]   DERMAL CYLINDROMA (TURBAN TUMOR) [J].
GIVEN, K ;
PICKRELL, K ;
SMITH, D .
PLASTIC AND RECONSTRUCTIVE SURGERY, 1977, 59 (04) :582-587