A DIRECT EVIDENCE FOR DEFECT IN GLUCOSE-6-PHOSPHATE TRANSPORT-SYSTEM IN HEPATIC-MICROSOMAL MEMBRANE OF GLYCOGEN-STORAGE DISEASE TYPE-IB

被引:39
作者
IGARASHI, Y [1 ]
KATO, S [1 ]
NARISAWA, K [1 ]
TADA, K [1 ]
AMANO, Y [1 ]
MORI, T [1 ]
TAKEUCHI, S [1 ]
机构
[1] SHINSHU UNIV,SCH MED,DEPT PEDIAT,MATSUMOTO,NAGANO 390,JAPAN
关键词
D O I
10.1016/S0006-291X(84)80290-9
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:593 / 597
页数:5
相关论文
共 11 条
[1]   INVOLVEMENT OF A GLUCOSE-6-PHOSPHATE TRANSPORT-SYSTEM IN FUNCTION OF MICROSOMAL GLUCOSE 6-PHOSPHATASE [J].
ARION, WJ ;
WALLIN, BK ;
LANGE, AJ ;
BALLAS, LM .
MOLECULAR AND CELLULAR BIOCHEMISTRY, 1975, 6 (02) :75-83
[2]  
ARION WJ, 1980, J BIOL CHEM, V255
[3]   NEUTROPENIA AND IMPAIRED NEUTROPHIL MIGRATION IN TYPE-IB GLYCOGEN-STORAGE DISEASE [J].
BEAUDET, AL ;
ANDERSON, DC ;
MICHELS, VV ;
ARION, WJ ;
LANGE, AJ .
JOURNAL OF PEDIATRICS, 1980, 97 (06) :906-910
[4]  
IGARASHI Y, 1979, J INHERIT METAB DIS, V2, P45
[5]   SIMPLE PROCEDURE FOR ISOLATION OF RAT LIVER MICROSOMES [J].
KAMATH, SA ;
KUMMEROW, FA ;
NARAYAN, KA .
FEBS LETTERS, 1971, 17 (01) :90-&
[6]  
LANGE AJ, 1980, J BIOL CHEM, V255, P8381
[7]  
LOWRY OH, 1951, J BIOL CHEM, V193, P265
[8]   GLYCOGEN-STORAGE DISEASE TYPE-1B DUE TO A DEFECT OF GLUCOSE-6-PHOSPHATE TRANSLOCASE [J].
NARISAWA, K ;
OTOMO, H ;
IGARASHI, Y ;
ARAI, N ;
OTAKE, M ;
TADA, K ;
KUZUYA, T .
JOURNAL OF INHERITED METABOLIC DISEASE, 1982, 5 (04) :227-228
[9]   GLYCOGEN-STORAGE DISEASE TYPE-1B - MICROSOMAL GLUCOSE-6-PHOSPHATASE SYSTEM IN 2 PATIENTS WITH DIFFERENT CLINICAL FINDINGS [J].
NARISAWA, K ;
OTOMO, H ;
IGARASHI, Y ;
ARAI, N ;
OTAKE, M ;
TADA, K ;
KUZUYA, T .
PEDIATRIC RESEARCH, 1983, 17 (07) :545-549
[10]   NEW VARIANT OF GLYCOGEN-STORAGE DISEASE TYPE-I PROBABLY DUE TO A DEFECT IN GLUCOSE-6-PHOSPHATE TRANSPORT-SYSTEM [J].
NARISAWA, K ;
IGARASHI, Y ;
OTOMO, H ;
TADA, K .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1978, 83 (04) :1360-1364