GRAY PLATELET SYNDROME - STUDIES ON PLATELET ALPHA-GRANULES, LYSOSOMES AND DEFECTIVE RESPONSE TO THROMBIN

被引:30
作者
SRIVASTAVA, PC
POWLING, MJ
NOKES, TJC
PATRICK, AD
DAWES, J
HARDISTY, RM
机构
[1] HOSP SICK CHILDREN,DEPT HAEMATOL ONCOL,GREAT ORMOND ST,LONDON WC1N 3JH,ENGLAND
[2] BURTON DIST HOSP,DEPT HAEMATOL,BURTON,ENGLAND
[3] BURTON DIST HOSP,DEPT HAEMATOL ONCOL,BURTON,ENGLAND
[4] MRC,SNBTS BLOOD COMPONENTS ASSAY GRP,EDINBURGH,SCOTLAND
[5] BURTON DIST HOSP,INST CHILD HLTH,DEPT CLIN BIOCHEM,BURTON,ENGLAND
关键词
D O I
10.1111/j.1365-2141.1987.tb04147.x
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:441 / 446
页数:6
相关论文
共 26 条
[1]   INOSITOL TRISPHOSPHATE, A NOVEL 2ND MESSENGER IN CELLULAR SIGNAL TRANSDUCTION [J].
BERRIDGE, MJ ;
IRVINE, RF .
NATURE, 1984, 312 (5992) :315-321
[2]   3 APPROACHES TO RADIOIMMUNOASSAY OF HUMAN BETA-THROMBOGLOBULIN [J].
BOLTON, AE ;
LUDLAM, CA ;
MOORE, S ;
PEPPER, DS ;
CASH, JD .
BRITISH JOURNAL OF HAEMATOLOGY, 1976, 33 (02) :233-238
[3]   CASE OF GM2 GANGLIOSIDOSIS OF LATE ONSET [J].
BUXTON, P ;
YOUNG, EP ;
ELLIS, RB ;
CUMINGS, JN ;
MAIR, WGP ;
ROBERTS, JR ;
LAKE, BD .
JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 1972, 35 (05) :685-&
[4]   RELEASE, DISTRIBUTION, AND CLEARANCE OF HUMAN BETA-THROMBOGLOBULIN AND PLATELET FACTOR-4 [J].
DAWES, J ;
SMITH, RC ;
PEPPER, DS .
THROMBOSIS RESEARCH, 1978, 12 (05) :851-861
[5]   A RADIOIMMUNOASSAY FOR THROMBOSPONDIN, USED IN A COMPARATIVE-STUDY OF THROMBOSPONDIN, BETA-THROMBOGLOBULIN AND PLATELET FACTOR-4 IN HEALTHY-VOLUNTEERS [J].
DAWES, J ;
CLEMETSON, KJ ;
GOGSTAD, GO ;
MCGREGOR, J ;
CLEZARDIN, P ;
PROWSE, CV ;
PEPPER, DS .
THROMBOSIS RESEARCH, 1983, 29 (06) :569-581
[6]   RAPID, SENSITIVE MICROASSAY FOR PLATELET 5HT [J].
DRUMMOND, AH ;
GORDON, JL .
THROMBOSIS ET DIATHESIS HAEMORRHAGICA, 1974, 31 (02) :366-367
[7]   BINDING OF SOLUBLE FORM OF FIBROBLAST SURFACE PROTEIN, FIBRONECTIN, TO COLLAGEN [J].
ENGVALL, E ;
RUOSLAHTI, E .
INTERNATIONAL JOURNAL OF CANCER, 1977, 20 (01) :1-5
[8]   BIOCHEMICAL-STUDIES OF 2 PATIENTS WITH THE GRAY PLATELET SYNDROME - SELECTIVE DEFICIENCY OF PLATELET ALPHA GRANULES [J].
GERRARD, JM ;
PHILLIPS, DR ;
RAO, GHR ;
PLOW, EF ;
WALZ, DA ;
ROSS, R ;
HARKER, LA ;
WHITE, JG .
JOURNAL OF CLINICAL INVESTIGATION, 1980, 66 (01) :102-109
[9]  
GLASESR JH, 1973, J LABORATORY CLIN ME, V32, P969
[10]   STUDIES OF PLATELETS FROM PATIENTS WITH THE GREY PLATELET SYNDROME [J].
GREENBERGSEPERSKY, SM ;
SIMONS, ER ;
WHITE, JG .
BRITISH JOURNAL OF HAEMATOLOGY, 1985, 59 (04) :603-609