HEPATOCELLULAR-CARCINOMA ASSOCIATED WITH ARTERIOHEPATIC DYSPLASIA IN A 4-YEAR-OLD GIRL

被引：22

作者：

BEKASSY, AN

GARWICZ, S

WIEBE, T

HAGERSTRAND, I

JENSEN, OA

机构：

[1] UNIV LUND HOSP,DEPT CLIN PATHOL,S-22185 LUND,SWEDEN

[2] UNIV COPENHAGEN,INST EYE PATHOL,DK-1168 COPENHAGEN,DENMARK

来源：

MEDICAL AND PEDIATRIC ONCOLOGY | 1992年 / 20卷 / 01期

关键词：

ALAGILLE SYNDROME; CHILD; HEPATIC CARCINOMA; LIVER CIRRHOSIS; BILIARY ATRESIA; AUTOPSY; HISTOPATHOLOGY; EYES; LIVER; AFP;

D O I：

10.1002/mpo.2950200118

中图分类号：

R73 [肿瘤学];

学科分类号：

100214 ;

摘要：

Hepatocellular carcinoma and obliterated hepatic bile duct were found at post-mortem examination in a 4-year-old girl with arteriohepatic dysplasia (Alagille's syndrome). AFP level was extremely high. Liver cirrhosis was present on percutaneous needle biopsy 9 months before she succumbed in progressive liver failure. Episodes of repeated gastrointestinal, life-threatening hemorrhages occurred during the last 6 months of her life. Histopathologic findings of the eyes were documented at autopsy.

引用

页码：78 / 83

页数：6

共 26 条

[1] HEPATOCELLULAR-CARCINOMA ASSOCIATED WITH ARTERIOHEPATIC DYSPLASIA [J].

ADAMS, PC .

DIGESTIVE DISEASES AND SCIENCES, 1986, 31 (04) :438-442

[2] HEPATIC DUCTULAR HYPOPLASIA ASSOCIATED WITH CHARACTERISTIC FACIES, VERTEBRAL MALFORMATIONS, RETARDED PHYSICAL, MENTAL AND SEXUAL DEVELOPMENT, AND CARDIAC MURMUR [J].

ALAGILLE, D ;

ODIEVRE, M ;

GAUTIER, M ;

DOMMERGUES, JP .

JOURNAL OF PEDIATRICS, 1975, 86 (01) :63-71

[3]

Alagille D, 1969, J PEDIAT, V301, P301

[4]

BEKASSY NA, 1984, ADV COURSE LIVER DIS

[5] INTRA-HEPATIC CHOLESTASIS FOR 15 YEARS WITHOUT CIRRHOSIS [J].

BRANSKI, D ;

LEBENTHAL, E ;

HATCH, TF ;

BALIAH, T ;

ROSENFELD, G .

JOURNAL OF CLINICAL GASTROENTEROLOGY, 1980, 2 (03) :251-257

[6]

DAHMS BB, 1982, HEPATOLOGY, V2, P350

[7]

DAHMS BB, 1979, ARCH PATHOL LAB MED, V103, P30

[8]

DEORAS MP, 1968, ARCH PATHOL, V86, P338

[9] FAMILIAL INTRAHEPATIC CHOLESTATIC CIRRHOSIS IN YOUNG-ADULTS [J].

HARATAKE, J ;

HORIE, A ;

ISHII, N ;

OKUNO, F .

GASTROENTEROLOGY, 1985, 89 (01) :202-209

[10] HEPATOCARCINOMA IN A CHILD WITH THE ALAGILLE SYNDROME [J].

KAUFMAN, SS ;

WOOD, RP ;

SHAW, BW ;

MARKIN, RS ;

GRIDELLI, B ;

VANDERHOOF, JA .

AMERICAN JOURNAL OF DISEASES OF CHILDREN, 1987, 141 (06) :698-700

← 1 2 3 →