PREPARATION OF GLUCOCEREBROSIDE BETA-GLUCOSIDASE FOR ENTRAPMENT IN LIPOSOMES AND TREATMENT OF PATIENTS WITH ADULT GAUCHERS-DISEASE

被引:23
作者
BRAIDMAN, I [1 ]
GREGORIADIS, G [1 ]
机构
[1] CLIN RES CTR,DIV CLIN INVEST,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
关键词
D O I
10.1042/bst0040259
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:259 / 261
页数:3
相关论文
共 6 条
[1]   METABOLISM OF GLUCOCEREBROSIDES .2. EVIDENCE OF AN ENZYMATIC DEFICIENCY IN GAUCHERS DISEASE [J].
BRADY, RO ;
KANFER, JN ;
SHAPIRO, D .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1965, 18 (02) :221-&
[2]   REPLACEMENT THERAPY FOR INHERITED ENZYME DEFICIENCY - USE OF PURIFIED GLUCOCEREBROSIDASE IN GAUCHERS-DISEASE [J].
BRADY, RO ;
PENTCHEV, PG ;
GAL, AE ;
HIBBERT, SR ;
DEKABAN, AS .
NEW ENGLAND JOURNAL OF MEDICINE, 1974, 291 (19) :989-993
[3]   ENZYME-CONTAINING LIPOSOMES ALLEVIATE A MODEL FOR STORAGE DISEASE [J].
GREGORIADIS, G ;
BUCKLAND, RA .
NATURE, 1973, 244 (5412) :170-172
[4]   DRUG-CARRIER POTENTIAL OF LIPOSOMES IN CANCER CHEMOTHERAPY [J].
GREGORIADIS, G ;
WILLS, EJ ;
SWAIN, CP ;
TAVILL, AS .
LANCET, 1974, 1 (7870) :1313-1316
[5]  
Gregoriadis G, 1974, ENZYME THERAPY LYSOS, P131
[6]   IDENTITY OF ACID BETA-GLUCOSIDASE AND GLUCOCEREBROSIDASE IN HUMAN SPLEEN [J].
HO, MW .
BIOCHEMICAL JOURNAL, 1973, 136 (03) :721-729