NEOPLASMS IN PROTEUS SYNDROME

被引：61

作者：

GORDON, PL

WILROY, RS

LASATER, OE

COHEN, MM

机构：

[1] DALHOUSIE UNIV, FAC DENT, DEPT ORAL BIOL, HALIFAX, NS B3H 3J5, CANADA

[2] UNIV TENNESSEE, DIV GENET, MEMPHIS, TN USA

[3] UNIV TENNESSEE, DEPT PEDIAT PATHOL, MEMPHIS, TN USA

[4] DALHOUSIE UNIV, FAC MED, DEPT PEDIAT, HALIFAX, NS B3H 3J5, CANADA

来源：

AMERICAN JOURNAL OF MEDICAL GENETICS | 1995年 / 57卷 / 01期

关键词：

TUMORS; MESOTHELIOMA; SEROUS CYSTADENOMA;

D O I：

10.1002/ajmg.1320570117

中图分类号：

Q3 [遗传学];

学科分类号：

071007 [遗传学]; 090102 [作物遗传育种];

摘要：

We report on 2 children with Proteus syndrome who developed neoplasms. Patient 1 had a probable mesothelioma, although papillary carcinoma of the thyroid could not be completely ruled out. Patient 2 had bilateral ovarian serous cystadenomas with nuclear atypia. Other unusual neoplasms in Proteus syndrome are discussed, together with their etiologic and pathogenetic possibilities. (C) 1995 Wiley-Liss, Inc.

引用

页码：74 / 78

页数：5

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