DELAYED POSTANOXIC DEMYELINATION AND ARYLSULFATASE-A PSEUDODEFICIENCY

被引：43

作者：

WEINBERGER, LM

SCHMIDLEY, JW

SCHAFER, IA

RAGHAVAN, S

机构：

[1] CASE WESTERN RESERVE UNIV,SCH MED,DEPT NEUROL,CLEVELAND,OH 44106

[2] NYU,SCH MED,DEPT NEUROL,NEW YORK,NY

[3] CASE WESTERN RESERVE UNIV,SCH MED,DEPT PEDIAT,CLEVELAND,OH 44106

来源：

NEUROLOGY | 1994年 / 44卷 / 01期

关键词：

D O I：

10.1212/WNL.44.1.152

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

We report a patient with delayed postanoxic demyelination who had pseudodeficiency of arylsulfatase A, reducing his enzyme activity to 10 to 30% of normal. This may have implications regarding the pathogenesis of postanoxic demyelination.

引用

页码：152 / 154

页数：3

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