HYPERCALCIURIA AND NEPHROCALCINOSIS, A FEATURE OF WILSONS-DISEASE

被引:21
作者
HOPPE, B [1 ]
NEUHAUS, T [1 ]
SUPERTIFURGA, A [1 ]
FORSTER, I [1 ]
LEUMANN, E [1 ]
机构
[1] UNIV ZURICH,CHILDRENS HOSP,STEINWIESSTR 75,CH-8032 ZURICH,SWITZERLAND
来源
NEPHRON | 1993年 / 65卷 / 03期
关键词
WILSONS DISEASE; HYPERCALCIURIA; OXALATE EXCRETION; NEPHROCALCINOSIS; NEPHROLITHIASIS;
D O I
10.1159/000187530
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 [临床医学]; 100201 [内科学];
摘要
Hypercalciuria and nephrocalcinosis are not uncommon in patients with Wilson's disease but have only once been reported as the presenting sign. We diagnosed Wilson's disease in a 17-year-old male patient 6 years after his first episode of gross hematuria and 2 years after detection of hypercalciuria and nephrocalcinosis. Therapy with penicillamine resulted only in a moderate reduction of urinary calcium excretion but oxalate excretion increased.
引用
收藏
页码:460 / 462
页数:3
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