ATYPICAL MR PRESENTATION OF WILSON DISEASE - A POSSIBLE CONSEQUENCE OF PARAMAGNETIC EFFECT OF COPPER

被引:26
作者
BRUGIERES, P
COMBES, C
RICOLFI, F
DEGOS, JD
POIRIER, J
GASTON, A
机构
[1] UNIV PARIS 12,HENRI MONDOR HOSP,DEPT NEUROL,F-94010 CRETEIL,FRANCE
[2] UNIV PARIS 12,HENRI MONDOR HOSP,DEPT PATHOL,F-94010 CRETEIL,FRANCE
关键词
WILSON DISEASE; MR STUDY;
D O I
10.1007/BF00596341
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A 53-year-old patient with Wilsons's disease and without autonomic dysfunction presented on T2-weighted MR study an atypical decreased signal intensity of the putamina and the caudate nuclei. Possible explanations of such a signal abnormalities are discussed.
引用
收藏
页码:222 / 224
页数:3
相关论文
共 8 条
[1]   PARKINSON PLUS SYNDROME - DIAGNOSIS USING HIGH-FIELD MR IMAGING OF BRAIN IRON [J].
DRAYER, BP ;
OLANOW, W ;
BURGER, P ;
JOHNSON, GA ;
HERFKENS, R ;
RIEDERER, S .
RADIOLOGY, 1986, 159 (02) :493-498
[2]  
HUK WJ, 1989, CONGENITAL CAUSES WI, P213
[3]   NUCLEAR MAGNETIC-RESONANCE (NMR) IMAGING IN WILSON DISEASE [J].
LAWLER, GA ;
PENNOCK, JM ;
STEINER, RE ;
JENKINS, WJ ;
SHERLOCK, S ;
YOUNG, IR .
JOURNAL OF COMPUTER ASSISTED TOMOGRAPHY, 1983, 7 (01) :1-8
[4]   MULTIPLE SYSTEM ATROPHY (SHY-DRAGER SYNDROME) - MR IMAGING [J].
PASTAKIA, B ;
POLINSKY, R ;
DICHIRO, G ;
SIMMONS, JT ;
BROWN, R ;
WENER, L .
RADIOLOGY, 1986, 159 (02) :499-502
[5]   IMPROVEMENT OF CEREBRAL CT ABNORMALITIES FOLLOWING LIVER-TRANSPLANTATION IN A PATIENT WITH WILSON DISEASE [J].
ROTHFUS, WE ;
HIRSCH, WL ;
MALATACK, JJ ;
BERGMAN, I .
JOURNAL OF COMPUTER ASSISTED TOMOGRAPHY, 1988, 12 (01) :138-140
[6]   NUCLEAR MAGNETIC-RESONANCE OF IRON AND COPPER DISEASE STATES [J].
RUNGE, VM ;
CLANTON, JA ;
SMITH, FW ;
HUTCHISON, J ;
MALLARD, J ;
PARTAIN, CL ;
JAMES, AE .
AMERICAN JOURNAL OF ROENTGENOLOGY, 1983, 141 (05) :943-948
[7]   CLINICAL-ASSESSMENT OF 31 PATIENTS WITH WILSONS-DISEASE - CORRELATIONS WITH STRUCTURAL-CHANGES ON MAGNETIC-RESONANCE-IMAGING [J].
STAROSTARUBINSTEIN, S ;
YOUNG, AB ;
KLUIN, K ;
HILL, G ;
AISEN, AM ;
GABRIELSEN, T ;
BREWER, GJ .
ARCHIVES OF NEUROLOGY, 1987, 44 (04) :365-370
[8]  
1976, GREENFIELDS NEUROPAT, P172