GROUP-C NIEMANN-PICK DISEASE - FAULTY REGULATION OF LOW-DENSITY-LIPOPROTEIN UPTAKE AND CHOLESTEROL STORAGE IN CULTURED FIBROBLASTS

被引：170

作者：

PENTCHEV, PG

COMLY, ME

KRUTH, HS

TOKORO, T

BUTLER, J

SOKOL, J

FILLINGKATZ, M

QUIRK, JM

MARSHALL, DC

PATEL, S

VANIER, MT

BRADY, RO

机构：

[1] FAC MED LYON SUD,INSERM,U189,BIOCHIM LAB,F-69921 OULLINS,FRANCE

[2] NHLBI,EXPTL ATHEROSCLEROSIS LAB,BETHESDA,MD 20892

[3] NICHHD,HUMAN GENET BRANCH,BETHESDA,MD 20892

[4] VET ADM MED CTR,NEUROL SERV,NEWINGTON,CT 06111

来源：

关键词：

D O I：

10.1096/fasebj.1.1.3609608

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：40 / 45

页数：6

共 15 条

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COMLY, ME
KRUTH, HS
VANIER, MT
WENGER, DA
PATEL, S
BRADY, RO
[J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1985, 82 (23) : 8247 - 8251