ACID BETA-GALACTOSIDASE FROM HUMAN-FIBROBLASTS - A MICROSCALE PURIFICATION METHOD MONITORED BY A HIGHLY SENSITIVE ENZYME ASSAY

被引：3

作者：

FURUYA, T

SUZUKI, Y

MOMOI, T

机构：

[1] UNIV TOKYO,FAC MED,DEPT PEDIAT,BUNKYO KU,TOKYO 113,JAPAN

[2] NATL CTR NERVOUS MENTAL & MUSCULAR DISORDERS,DIV CHEM PATHOL,KODAIRA,TOKYO 187,JAPAN

来源：

JOURNAL OF BIOCHEMISTRY | 1986年 / 99卷 / 02期

关键词：

D O I：

10.1093/oxfordjournals.jbchem.a135497

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：437 / 443

页数：7

共 13 条

[1]

BRADFORD MM, 1976, ANAL BIOCHEM, V72, P248, DOI 10.1016/0003-2697(76)90527-3

[2] MOLECULAR DEFECT IN COMBINED BETA-GALACTOSIDASE AND NEURAMINIDASE DEFICIENCY IN MAN [J].

DAZZO, A ;

HOOGEVEEN, A ;

REUSER, AJJ ;

ROBINSON, D ;

GALJAARD, H .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (15) :4535-4539

[3] CHARACTERIZATION OF PURIFIED HUMAN LIVER ACID BETA-D-GALACTOSIDASE-A2 AND GALACTOSIDASE-A3 [J].

FROST, RG ;

HOLMES, EW ;

NORDEN, AGW ;

OBRIEN, JS .

BIOCHEMICAL JOURNAL, 1978, 175 (01) :181-188

[4] GM1-GANGLIOSIDOSIS - A MOLECULAR ABNORMALITY OF ACID BETA-GALACTOSIDASE IN FIBROBLASTS [J].

FURUYA, T ;

SUZUKI, Y .

JOURNAL OF INHERITED METABOLIC DISEASE, 1984, 7 (03) :145-146

[5]

HASILIK A, 1980, J BIOL CHEM, V255, P4937

[6]

HOOGEVEEN AT, 1984, J BIOL CHEM, V259, P1974

[7] The determination of enzyme dissociation constants [J].

Lineweaver, H ;

Burk, D .

JOURNAL OF THE AMERICAN CHEMICAL SOCIETY, 1934, 56 :658-666

[8] CHARACTERIZATION OF A NEW HUMAN DIPLOID CELL STRAIN, IMR-90 [J].

NICHOLS, WW ;

MURPHY, DG ;

CRISTOFALO, VJ ;

TOJI, LH ;

GREENE, AE ;

DWIGHT, SA .

SCIENCE, 1977, 196 (4285) :60-63

[9]

OBRIEN JS, 1983, METABOLIC BASIS INHE, P945

[10] GENERALIZED GANGLIOSIDOSIS - BETA-GALACTOSIDASE DEFICIENCY [J].

OKADA, S ;

OBRIEN, JS .

SCIENCE, 1968, 160 (3831) :1002-&

← 1 2 →