COLLAGEN STUDIES IN CONGENITAL CUTIS LAXA

被引:10
作者
TAIEB, A
AUMAILLEY, M
COUROUGEDORCIER, D
RABAUD, M
BIOULACSAGE, P
SURLEVEBAZEILLE, JE
MALEVILLE, J
机构
[1] UNIV BORDEAUX 1,DEPT PEDIAT DERMATOL,F-33405 TALENCE,FRANCE
[2] UNIV BORDEAUX 1,DEPT ELECTRON MICROSCOPY,F-33405 TALENCE,FRANCE
[3] UNIV BORDEAUX 2,F-33076 BORDEAUX,FRANCE
[4] LAB RECH CARDIOL,PESSAC,FRANCE
关键词
D O I
10.1007/BF00431223
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
引用
收藏
页码:308 / 314
页数:7
相关论文
共 30 条
[1]  
ANDERSON CE, 1984, J PEDIATR-US, V105, P247, DOI 10.1016/S0022-3476(84)80121-3
[2]  
ANDERSON LL, 1985, J LAB CLIN MED, V105, P537
[3]   INFLUENCE OF CELL-DENSITY ON COLLAGEN BIOSYNTHESIS IN FIBROBLAST-CULTURES [J].
AUMAILLEY, M ;
KRIEG, T ;
RAZAKA, G ;
MULLER, PK ;
BRICAUD, H .
BIOCHEMICAL JOURNAL, 1982, 206 (03) :505-510
[4]   BIOCHEMICAL AND IMMUNOLOGICAL STUDIES OF FIBROBLASTS DERIVED FROM A PATIENT WITH EHLERS-DANLOS SYNDROME TYPE-IV DEMONSTRATE REDUCED TYPE-III COLLAGEN-SYNTHESIS [J].
AUMAILLEY, M ;
KRIEG, T ;
DESSAU, W ;
MULLER, PK ;
TIMPL, R ;
BRICAUD, H .
ARCHIVES OF DERMATOLOGICAL RESEARCH, 1980, 269 (02) :169-177
[5]   MEASUREMENT OF COLLAGEN-FIBER DIAMETER IN HUMAN-SKIN [J].
BARTON, SP ;
MARKS, R .
JOURNAL OF CUTANEOUS PATHOLOGY, 1984, 11 (01) :18-26
[6]   DOMINANT AND RECESSIVE FORMS CUTIS LAXA [J].
BEIGHTON, P .
JOURNAL OF MEDICAL GENETICS, 1972, 9 (02) :216-&
[7]  
BRADFORD MM, 1976, ANAL BIOCHEM, V72, P248, DOI 10.1016/0003-2697(76)90527-3
[8]   X-LINKED CUTIS LAXA - DEFECTIVE CROSS-LINK FORMATION IN COLLAGEN DUE TO DECREASED LYSYL OXIDASE ACTIVITY [J].
BYERS, PH ;
SIEGEL, RC ;
HOLBROOK, KA ;
NARAYANAN, AS ;
BORNSTEIN, P ;
HALL, JG .
NEW ENGLAND JOURNAL OF MEDICINE, 1980, 303 (02) :61-65
[9]   CHARACTERIZATION OF A TYPE-VI COLLAGEN-RELATED MR-140000 PROTEIN FROM CUTIS-LAXA FIBROBLASTS IN CULTURE [J].
CRAWFORD, SW ;
FEATHERSTONE, JA ;
HOLBROOK, K ;
YONG, SL ;
BORNSTEIN, P ;
SAGE, H .
BIOCHEMICAL JOURNAL, 1985, 227 (02) :491-502
[10]  
Ferreira M C, 1973, Br J Plast Surg, V26, P283, DOI 10.1016/0007-1226(73)90016-7