ALPHA-THALASSEMIA CHANGES ERYTHROCYTE HETEROGENEITY IN SICKLE-CELL DISEASE

被引:56
作者
NOGUCHI, CT
DOVER, GJ
RODGERS, GP
SERJEANT, GR
ANTONARAKIS, SE
ANAGNOU, NP
HIGGS, DR
WEATHERALL, DJ
SCHECHTER, AN
机构
[1] NHLBI,CLIN HEMATOL CLIN,BETHESDA,MD 20205
[2] JOHNS HOPKINS UNIV,SCH MED,DEPT MED,BALTIMORE,MD 21205
[3] JOHNS HOPKINS UNIV,SCH MED,DEPT PEDIAT,BALTIMORE,MD 21205
[4] UNIV W INDIES,MRC LABS,KINGSTON,JAMAICA
[5] UNIV OXFORD,JOHN RADCLIFFE HOSP,NUFFIELD DEPT CLIN MED,MOLEC HEMATOL UNIT,MRC,OXFORD OX3 9DU,ENGLAND
关键词
D O I
10.1172/JCI111870
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:1632 / 1637
页数:6
相关论文
共 41 条
[1]   GENETIC-DISEASES - DIAGNOSIS BY RESTRICTION ENDONUCLEASE ANALYSIS [J].
ANTONARAKIS, SE ;
PHILLIPS, JA ;
KAZAZIAN, HH .
JOURNAL OF PEDIATRICS, 1982, 100 (06) :845-856
[2]   IRREVERSIBLY SICKLED ERYTHROCYTES - A CONSEQUENCE OF HETEROGENOUS DISTRIBUTION OF HEMOGLOBIN TYPES IN SICKLE-CELL ANEMIA [J].
BERTLES, JF ;
MILNER, PFA .
JOURNAL OF CLINICAL INVESTIGATION, 1968, 47 (08) :1731-&
[3]  
BRITTENHAM GM, 1985, BLOOD, V65, P183
[4]  
BUNN HF, 1976, J CLIN INVEST, V57, P1652
[5]  
BUNN HF, 1977, HUMAN HEMOGLOBINS, P228
[6]  
CLARK MR, 1976, BLOOD, V48, P899
[7]   DEFORMABILITY OF OXYGENATED IRREVERSIBLY SICKLED CELLS [J].
CLARK, MR ;
MOHANDAS, N ;
SHOHET, SB .
JOURNAL OF CLINICAL INVESTIGATION, 1980, 65 (01) :189-196
[8]  
CORASH LM, 1974, J LAB CLIN MED, V84, P147
[9]  
DANON D, 1964, J LAB CLIN MED, V64, P668
[10]   SICKLE-CELL-ANEMIA - MOLECULAR AND CELLULAR BASES OF THERAPEUTIC APPROACHES .3. [J].
DEAN, J ;
SCHECHTER, AN .
NEW ENGLAND JOURNAL OF MEDICINE, 1978, 299 (16) :863-870