INDEPENDENCE OF TRIACYLGLYCEROL-CONTAINING COMPARTMENTS IN CULTURED FIBROBLASTS FROM WOLMAN DISEASE AND MULTISYSTEMIC LIPID STORAGE MYOPATHY

被引：18

作者：

SALVAYRE, R

NEGRE, A

RADOM, J

DOUSTEBLAZY, L

机构：

[1] UNIV TOULOUSE 3,FAC MED,BIOCHIM LAB,F-31062 TOULOUSE,FRANCE

[2] UNIV TOULOUSE 3,FAC MED,INSERM,U101,F-31062 TOULOUSE,FRANCE

来源：

FEBS LETTERS | 1989年 / 250卷 / 01期

关键词：

D O I：

10.1016/0014-5793(89)80679-9

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：35 / 39

页数：5

共 26 条

[1] MULTISYSTEM TRIGLYCERIDE STORAGE DISORDER WITH IMPAIRED LONG-CHAIN FATTY-ACID OXIDATION [J].

ANGELINI, C ;

PHILIPPART, M ;

BORRONE, C ;

BRESOLIN, N ;

CANTINI, M ;

LUCKE, S .

ANNALS OF NEUROLOGY, 1980, 7 (01) :5-10

[2]

BROWN MS, 1976, J BIOL CHEM, V251, P3277

[3] CHOLESTEROL ESTER AND TRIGLYCERIDE-METABOLISM IN INTACT FIBROBLASTS FROM PATIENTS WITH WOLMANS DISEASE AND CHOLESTEROL ESTER STORAGE DISEASE [J].

BURTON, BK ;

REMY, WT ;

RAYMAN, L .

PEDIATRIC RESEARCH, 1984, 18 (12) :1242-1245

[4] NEUTRAL LIPID STORAGE DISEASE - NEW DISORDER OF LIPID-METABOLISM [J].

CHANARIN, I ;

PATEL, A ;

SLAVIN, G ;

WILLS, EJ ;

ANDREWS, TM ;

STEWART, G .

BRITISH MEDICAL JOURNAL, 1975, 1 (5957) :553-555

[5]

FOLCH J, 1957, J BIOL CHEM, V226, P497

[6]

GOLDSTEIN JL, 1974, J BIOL CHEM, V249, P5153

[7]

GOLDSTEIN JL, 1975, J BIOL CHEM, V250, P8487

[8]

GOLDSTEIN JL, 1980, J BIOL CHEM, V255, P1839

[9]

GOLDSTEIN JL, 1983, METABOLIC BASIS INHE, P672

[10]

GREENSPAN P, 1984, J BIOL CHEM, V259, P1703

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