HARDEROPORPHYRIA - A VARIANT HEREDITARY COPROPORPHYRIA

被引:70
作者
NORDMANN, Y
GRANDCHAMP, B
DEVERNEUIL, H
PHUNG, L
CARTIGNY, B
FONTAINE, G
机构
关键词
D O I
10.1172/JCI111039
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:1139 / 1149
页数:11
相关论文
共 23 条
[1]  
BOYUM A, 1968, SCAND J CLIN LAB INV, VS 21, P77
[2]  
BRODIE MJ, 1977, Q J MED, V46, P229
[3]  
de Verneuil H, 1978, Hum Genet, V44, P145
[4]  
Elder G H, 1982, Semin Liver Dis, V2, P87, DOI 10.1055/s-2008-1040699
[5]  
ELDER GH, 1976, LANCET, V2, P1217
[6]   RADIOCHEMICAL METHOD FOR MEASUREMENT OF COPROPORPHYRINOGEN OXIDASE AND UTILIZATION OF SUBSTRATES OTHER THAN COPROPORPHYRINOGEN-III BY ENZYME FROM RAT-LIVER [J].
ELDER, GH ;
EVANS, JO .
BIOCHEMICAL JOURNAL, 1978, 169 (01) :205-214
[7]   FACTORS DETERMINING SEQUENCE OF OXIDATIVE DECARBOXYLATION OF 2-PROPIONATE AND 4-PROPIONATE SUBSTITUENTS OF COPROPORPHYRINOGEN-III BY COPROPORPHYRINOGEN OXIDASE IN RAT-LIVER [J].
ELDER, GH ;
EVANS, JO ;
JACKSON, JR ;
JACKSON, AH .
BIOCHEMICAL JOURNAL, 1978, 169 (01) :215-223
[8]  
FALK JE, 1964, PORPHYRINS METALLOPO, P231
[9]   COPROPORPHYRINOGEN-III OXIDASE ASSAY [J].
GRANDCHAMP, B ;
NORDMANN, Y .
ENZYME, 1982, 28 (2-3) :196-204
[10]  
GRANDCHAMP B, 1977, LANCET, V2, P1348