METHYLUMBELLIFERYL-N-ACETYLNEURAMINIC ACID SIALIDASE IN HUMAN-LIVER

被引:5
作者
DENTANDT, WR
SCHARPE, S
机构
来源
BIOCHEMICAL MEDICINE | 1984年 / 31卷 / 03期
关键词
D O I
10.1016/0006-2944(84)90084-X
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:287 / 293
页数:7
相关论文
共 16 条
[1]   CHARACTERIZATION OF HUMAN-LIVER (4-METHYLUMBELLIFERYL-ALPHA-D-N-ACETYLNEURAMINIC ACID) NEURAMINIDASE ACTIVITY [J].
ALHADEFF, JA ;
WOLFE, S .
INTERNATIONAL JOURNAL OF BIOCHEMISTRY, 1981, 13 (09) :975-980
[2]   LYSOSOMAL HYDROLASES IN CYSTIC-FIBROSIS LIVERS [J].
ALHADEFF, JA .
CLINICA CHIMICA ACTA, 1978, 89 (03) :469-473
[3]  
DENTANDT WR, 1980, HUM GENET, V55, P383
[4]  
HORVAT A, 1968, J BIOL CHEM, V243, P4380
[5]  
KISHORE GS, 1975, J BIOL CHEM, V250, P2655
[6]  
MAHADEVAN S, 1967, J BIOL CHEM, V242, P4409
[7]   HUMAN-LIVER NEURAMINIDASE [J].
MEYER, DM ;
LEMONNIER, M ;
BOURRILLON, R .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1981, 103 (04) :1302-1309
[8]  
MINAMI R, 1979, CLIN CHIM ACTA, V96, P107
[9]   NEURAMINIDASE IN CULTURED FIBROBLASTS AND LEUKOCYTES OF HOMOZYGOTES AND HETEROZYGOTES FOR THE MUCOLIPIDOSIS-II GENE (I-CELL DISEASE) [J].
POTIER, M ;
MELANCON, SB ;
DALLAIRE, L ;
CHICOINE, R ;
MAMELI, L ;
BELISLE, M .
AMERICAN JOURNAL OF MEDICAL GENETICS, 1979, 4 (02) :191-200
[10]   NEURAMINIDASE DEFICIENCY IN THE MOUSE [J].
POTIER, M ;
LUSHUNYAN, D ;
WOMACK, JE .
FEBS LETTERS, 1979, 108 (02) :345-348