FATTY-ACID ABNORMALITY IN ADRENOLEUKODYSTROPHY

被引:405
作者
IGARASHI, M
SCHAUMBURG, HH
POWERS, J
KISHIMOTO, Y
KOLODNY, E
SUZUKI, K
机构
[1] ALBERT EINSTEIN COLL MED ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN DEV,BRONX,NY 10461
[2] EUNICE KENNEDY SHRIVER CTR MENTAL RETARDATION,WALTHAM,MA 02154
[3] MED UNIV S CAROLINA,DEPT PATHOL,CHARLESTON,SC 29401
[4] ALBERT EINSTEIN COLL MED SAUL R KOREY DEPT NEUROL,BRONX,NY 10461
[5] ALBERT EINSTEIN COLL MED,DEPT NEUROSCI,BRONX,NY 10461
[6] ALBERT EINSTEIN COLL MED,DEPT PATHOL,BRONX,NY 10461
[7] ALBERT EINSTEIN COLL MED ROSE F KENNEDY CTR RES MENTAL RETARDATION & HUMAN DEV,BRONX,NY 10461
关键词
D O I
10.1111/j.1471-4159.1976.tb04462.x
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:851 / &
相关论文
共 38 条
[1]  
ABRAMSON MB, 1965, J BIOL CHEM, V240, P2389
[2]  
AGUILAR MJ, 1966, INBORN DISORDERS SPH, P149
[3]   CONCENTRATION AND FATTY ACID COMPOSITION OF CHOLESTERYL ESTERS OF NORMAL HUMAN BRAIN [J].
ALLING, C ;
SVENNERHOLM, L .
JOURNAL OF NEUROCHEMISTRY, 1969, 16 (05) :751-+
[4]  
Blaw M, 1970, HDB CLIN NEUROLOGY, V10, P128
[5]   SCHILDERS DISEASE - ABNORMAL CHOLESTEROL RETENTION AND ACCUMULATION IN CULTIVATED FIBROBLASTS [J].
BURTON, BK ;
NADLER, HL .
PEDIATRIC RESEARCH, 1974, 8 (03) :170-175
[6]  
CARROLL KK, 1961, J LIPID RES, V2, P135
[7]   SCHILDERS DISEASE (SUDANOPHILIC LEUCODYSTROPHY) IN 5 MALE MEMBERS OF 1 FAMILY [J].
CROME, L ;
ZAPELLA, M .
JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 1963, 26 (05) :431-+
[8]   SUDANOPHILIC LEUKODYSTROPHY WITH INCREASED HEXOSAMINE CONTENT [J].
DYCK, PJ ;
CUMINGS, JN ;
OLSZEWSKI, J .
NEUROLOGY, 1960, 10 (08) :765-771
[9]  
ETO Y, 1971, BIOCHIM BIOPHYS ACTA, V239, P293
[10]   CHOLESTEROL ESTERS IN DEVELOPING RAT-BRAIN - CONCENTRATION AND FATTY-ACID COMPOSITION [J].
ETO, Y ;
SUZUKI, K .
JOURNAL OF NEUROCHEMISTRY, 1972, 19 (01) :109-&