SITE OF AUTONOMIC DYSFUNCTION IN A PATIENT WITH ROSS SYNDROME AND POSTGANGLIONIC HORNERS-SYNDROME

被引:27
作者
WOLFE, GI [1 ]
GALETTA, SL [1 ]
TEENER, JW [1 ]
KATZ, JS [1 ]
BIRD, SJ [1 ]
机构
[1] UNIV PENN,MED CTR,DEPT NEUROL,PHILADELPHIA,PA 19104
关键词
D O I
10.1212/WNL.45.11.2094
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Ross' syndrome is a rare peripheral nervous system disorder defined by Adie's tonic pupil, hyporeflexia, and segmental anhidrosis. Injury to postganglionic cholinergic fibers is believed to account for the tonic pupil and sweating disturbance. We report 47-year-old man found to have Ross' syndrome in combination with a complete postganglionic Horner's syndrome. Pharmacologic and sudomotor tests in this unique patient provide further evidence that Ross' syndrome results from injury to sympathetic and parasympathetic ganglion cells or to their postganglionic projections.
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页码:2094 / 2096
页数:3
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