STUDIES OF THE RESIDUAL GLYCOGEN BRANCHING ENZYME-ACTIVITY PRESENT IN HUMAN-SKIN FIBROBLASTS FROM PATIENTS WITH TYPE-IV GLYCOGEN-STORAGE DISEASE

被引：24

作者：

BROWN, DH

BROWN, BI

机构：

来源：

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS | 1983年 / 111卷 / 02期

关键词：

D O I：

10.1016/0006-291X(83)90354-6

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：636 / 643

页数：8

共 12 条

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[3]

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[6] TYPE-IV GLYCOGEN STORAGE DISEASE - BRANCHING ENZYME DEFICIENCY IN SKIN FIBROBLASTS AND POSSIBLE HETEROZYGOTE DETECTION [J].

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[7]

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[8] STUDIES ON LEUKOCYTE BRANCHER ENZYME ACTIVITY IN A FAMILY WITH TYPE 4 GLYCOGENOSIS [J].

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NITOWSKY, HM .

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[9]

MANNERS DJ, 1967, CONTROL GLYCOGEN MET, P83

[10] PURIFICATION AND PROPERTIES OF RABBIT SKELETAL-MUSCLE GLYCOGEN SYNTHASE [J].

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