ACTIVITY OF PEROXISOMAL ENZYMES AND INTRACELLULAR-DISTRIBUTION OF CATALASE IN ZELLWEGER SYNDROME

被引:180
作者
WANDERS, RJA
KOS, M
ROEST, B
MEIJER, AJ
SCHRAKAMP, G
HEYMANS, HSA
TEGELAERS, WHH
VANDENBOSCH, H
SCHUTGENS, RBH
TAGER, JM
机构
[1] UNIV UTRECHT,BIOCHEM LAB,3584 CH UTRECHT,NETHERLANDS
[2] UNIV AMSTERDAM,BIOCHEM LAB,1018 TV AMSTERDAM,NETHERLANDS
关键词
D O I
10.1016/S0006-291X(84)80240-5
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:1054 / 1061
页数:8
相关论文
共 23 条
[21]   DEFICIENCY OF ACYL-COA-DIHYDROXYACETONE PHOSPHATE ACYLTRANSFERASE IN PATIENTS WITH ZELLWEGER (CEREBRO-HEPATO-RENAL) SYNDROME [J].
SCHUTGENS, RBH ;
ROMEYN, GJ ;
WANDERS, RJA ;
VANDENBOSCH, H ;
SCHRAKAMP, G ;
HEYMANS, HSA .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1984, 120 (01) :179-184
[22]   BIOCHEMICAL-STUDIES IN THE LIVER AND MUSCLE OF PATIENTS WITH ZELLWEGER SYNDROME [J].
TRIJBELS, JMF ;
BERDEN, JA ;
MONNENS, LAH ;
WILLEMS, JL ;
JANSSEN, AJM ;
SCHUTGENS, RBH ;
VANDENBROEKVANESSEN, M .
PEDIATRIC RESEARCH, 1983, 17 (06) :514-517
[23]  
WIEACKER P, 1980, ANN GENET-PARIS, V23, P73