SYNTHESIS AND PROCESSING OF ARYLSULFATASE-A IN HUMAN-SKIN FIBROBLASTS

被引:63
作者
WAHEED, A
HASILIK, A
VONFIGURA, K
机构
来源
HOPPE-SEYLERS ZEITSCHRIFT FUR PHYSIOLOGISCHE CHEMIE | 1982年 / 363卷 / 04期
关键词
D O I
10.1515/bchm2.1982.363.1.425
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:425 / 430
页数:6
相关论文
共 26 条
[1]   A CONTROLLED STUDY OF ENZYMIC ACTIVITIES IN 3 HUMAN DISORDERS OF GLYCOLIPID METABOLISM [J].
AUSTIN, JH ;
BALASUBRAMANIAN, AS ;
BACHHAWAT, BK ;
BASU, DK ;
SARASWATHI, S ;
PATTABIRAMAN, TN .
JOURNAL OF NEUROCHEMISTRY, 1963, 10 (11) :805-&
[2]   THE SYNTHESIS AND PROCESSING OF BETA-GLUCURONIDASE IN NORMAL AND EGASYN DEFICIENT MOUSE KIDNEY [J].
BROWN, JA ;
JAHREIS, GP ;
SWANK, RT .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1981, 99 (02) :691-699
[3]  
CANTZ M, 1972, METHOD ENZYMOL, V28, P884
[4]   VARIATION OF ARYLSULPHATASE-A - COMPARATIVE STUDIES OF ARYLSULFATASE A WITH SYNTHETIC AND NATURAL SUBSTRATES IN 3 FAMILIES WITH METACHROMATIC LEUCODYSTROPHY [J].
CHRISTOMANOU, H ;
SANDHOFF, K .
NEUROPADIATRIE, 1978, 9 (04) :385-395
[5]  
ERICKSON AH, 1979, J BIOL CHEM, V254, P1771
[6]  
FRISCH A, 1981, J BIOL CHEM, V256, P8242
[7]   TRANSPORT AND PROCESSING OF LYSOSOMAL-ENZYMES BY SMOOTH-MUSCLE CELLS AND ENDOTHELIAL-CELLS [J].
HASILIK, A ;
VOSS, B ;
VONFIGURA, K .
EXPERIMENTAL CELL RESEARCH, 1981, 133 (01) :23-30
[8]  
HASILIK A, 1980, J BIOL CHEM, V255, P4946
[9]   OLIGOSACCHARIDES IN LYSOSOMAL-ENZYMES - DISTRIBUTION OF HIGH-MANNOSE AND COMPLEX OLIGOSACCHARIDES IN CATHEPSIN D AND BETA-HEXOSAMINIDASE [J].
HASILIK, A ;
VONFIGURA, K .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1981, 121 (01) :125-129
[10]  
HASILIK A, 1980, J BIOL CHEM, V255, P4937