ABNORMAL OXIDANT SENSITIVITY AND BETA-CHAIN STRUCTURE OF SPECTRIN IN HEREDITARY SPHEROCYTOSIS ASSOCIATED WITH DEFECTIVE SPECTRIN-PROTEIN 4.1 BINDING

被引:56
作者
BECKER, PS
MORROW, JS
LUX, SE
机构
[1] CHILDRENS HOSP MED CTR,DIV HEMATOL ONCOL,ENDERS 7,300 LONGWOOD AVE,BOSTON,MA 02115
[2] HARVARD UNIV,SCH MED,BOSTON,MA 02115
[3] HARVARD UNIV,SCH MED,DANA FARBER CANC INST,BOSTON,MA 02115
[4] HARVARD UNIV,DIV MED SCI,PROGRAM CELL & DEV BIOL,BOSTON,MA 02115
[5] YALE UNIV,SCH MED,DEPT PATHOL,NEW HAVEN,CT 06510
关键词
D O I
10.1172/JCI113104
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:557 / 565
页数:9
相关论文
共 69 条
  • [1] DEFICIENT RED-CELL SPECTRIN IN SEVERE, RECESSIVELY INHERITED SPHEROCYTOSIS
    AGRE, P
    ORRINGER, EP
    BENNETT, V
    [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1982, 306 (19) : 1155 - 1161
  • [2] INHERITANCE PATTERN AND CLINICAL-RESPONSE TO SPLENECTOMY AS A REFLECTION OF ERYTHROCYTE SPECTRIN DEFICIENCY IN HEREDITARY SPHEROCYTOSIS
    AGRE, P
    ASIMOS, A
    CASELLA, JF
    MCMILLAN, C
    [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1986, 315 (25) : 1579 - 1583
  • [3] PARTIAL DEFICIENCY OF ERYTHROCYTE SPECTRIN IN HEREDITARY SPHEROCYTOSIS
    AGRE, P
    CASELLA, JF
    ZINKHAM, WH
    MCMILLAN, C
    BENNETT, V
    [J]. NATURE, 1985, 314 (6009) : 380 - 383
  • [4] SP-ALPHA-I/65 HEREDITARY ELLIPTOCYTOSIS IN NORTH-AFRICA
    ALLOISIO, N
    GUETARNI, D
    MORLE, L
    POTHIER, B
    DUCLUZEAU, MT
    SOUN, A
    COLONNA, P
    CLERC, M
    PHILIPPE, N
    DELAUNAY, J
    [J]. AMERICAN JOURNAL OF HEMATOLOGY, 1986, 23 (02) : 113 - 122
  • [5] GLYCOPHORIN IS LINKED BY BAND-4.1 PROTEIN TO THE HUMAN-ERYTHROCYTE MEMBRANE SKELETON
    ANDERSON, RA
    LOVRIEN, RE
    [J]. NATURE, 1984, 307 (5952) : 655 - 658
  • [6] BECKER PS, 1984, J CELL BIOL, V99, pA113
  • [7] HIGH-YIELD PURIFICATION OF PROTEIN 4.1 FROM HUMAN-ERYTHROCYTE MEMBRANES
    BECKER, PS
    SPIEGEL, JE
    WOLFE, LC
    LUX, SE
    [J]. ANALYTICAL BIOCHEMISTRY, 1983, 132 (01) : 195 - 201
  • [8] BECKER PS, 1986, J BIOL CHEM, V261, P4620
  • [9] BECKER PS, 1985, CLIN HAEMATOL, V14, P14
  • [10] BERNSTEIN SE, 1980, LAB ANIM SCI, V30, P197