MYOMETRY ASSESSMENT IN PATIENTS WITH DUCHENNE MUSCULAR-DYSTROPHY

被引:1
作者
ARAUJO, APQC
DURO, LA
ARAUJO, AQC
PENQUE, GMCA
机构
[1] UNIV FED RIO DE JANEIRO,DEPT PEDIAT,BR-22631020 RIO JANEIRO,BRAZIL
[2] UFRJ,INST NEUROL DEOLINDO COUTO,BR-22631020 RIO JANEIRO,BRAZIL
关键词
MUSCULAR FUNCTION; MYOMETRY; DUCHENNE MUSCULAR DYSTROPHY;
D O I
10.1590/S0004-282X1995000200008
中图分类号
Q189 [神经科学];
学科分类号
071006 ;
摘要
An account of the authors' experience in strength measurement using in strength measurement using a hand-held dynamometer in 16 patients with Duchenne muscular dystrophy (DMD) is given. A rapid decrease of knee extension strength was observed, between 6 and 8 years of age, analysing among patients of different ages. At the same time loss of the ability to walk has occurred. An unexplainable increase in strength was observed in two patients examined in a six month interval. A short review of the literature is given and the conclusion of the importance on the wider use of the instrument.
引用
收藏
页码:233 / 237
页数:5
相关论文
共 14 条
[1]  
ARAUJO AQC, 1990, ARQ NEUROPSIQUIATR S, V48
[2]   HUMAN SKELETAL-MUSCLE FUNCTION - DESCRIPTION OF TESTS AND NORMAL VALUES [J].
EDWARDS, RHT ;
YOUNG, A ;
HOSKING, GP ;
JONES, DA .
CLINICAL SCIENCE AND MOLECULAR MEDICINE, 1977, 52 (03) :283-290
[3]   PRACTICAL ANALYSIS OF VARIABILITY OF MUSCLE FUNCTION MEASUREMENTS IN DUCHENNE MUSCULAR-DYSTROPHY [J].
EDWARDS, RHT ;
CHAPMAN, SJ ;
NEWHAM, DJ ;
JONES, DA .
MUSCLE & NERVE, 1987, 10 (01) :6-14
[4]  
EDWARDS RHT, 1974, LANCET, V2, P757
[5]   MEASUREMENTS OF MUSCLE STRENGTH AND PERFORMANCE IN CHILDREN WITH NORMAL AND DISEASED MUSCLE [J].
HOSKING, GP ;
BHAT, US ;
DUBOWITZ, V ;
EDWARDS, RHT .
ARCHIVES OF DISEASE IN CHILDHOOD, 1976, 51 (12) :957-963
[6]  
Hyde S A, 1983, Physiotherapy, V69, P424
[7]  
KARNI Y, 1984, PHYSIOTHERAPY, V70, P282
[8]  
MESA LE, 1991, DISORD, V1, P261
[9]   THERAPEUTIC POSSIBILITIES OF CHRONIC LOW-FREQUENCY ELECTRICAL-STIMULATION IN CHILDREN WITH DUCHENNE MUSCULAR-DYSTROPHY [J].
SCOTT, OM ;
HYDE, SA ;
VRBOVA, G ;
DUBOWITZ, V .
JOURNAL OF THE NEUROLOGICAL SCIENCES, 1990, 95 (02) :171-182
[10]   QUANTITATION OF MUSCLE FUNCTION IN CHILDREN - A PROSPECTIVE-STUDY IN DUCHENNE MUSCULAR-DYSTROPHY [J].
SCOTT, OM ;
HYDE, SA ;
GODDARD, C ;
DUBOWITZ, V .
MUSCLE & NERVE, 1982, 5 (04) :291-301