N-ACETYLNEURAMINIC ACID AND SIALOGLYCOCONJUGATE METABOLISM IN FIBROBLASTS FROM A PATIENT WITH GENERALIZED N-ACETYLNEURAMINIC ACID STORAGE DISEASE

被引:26
作者
HANCOCK, LW
HORWITZ, AL
DAWSON, G
机构
[1] UNIV CHICAGO, PRITZKER SCH MED, JOSEPH P KENNEDY JR MENTAL RETARDAT RES CTR, DEPT PEDIAT, CHICAGO, IL 60637 USA
[2] UNIV CHICAGO, PRITZKER SCH MED, JOSEPH P KENNEDY JR MENTAL RETARDAT RES CTR, DEPT BIOCHEM, CHICAGO, IL 60637 USA
关键词
D O I
10.1016/0304-4165(83)90122-8
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:42 / 52
页数:11
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