METABOLISM OF BRANCHED-CHAIN FATTY-ACIDS IN PEROXISOMAL DISORDERS

被引：4

作者：

SINGH, H

USHER, S

JOHNSON, D

POULOS, A

机构：

[1] Department of Chemical Pathology, Adelaide Children's Hospital, North Adelaide, 5006, South Australia

来源：

JOURNAL OF INHERITED METABOLIC DISEASE | 1990年 / 13卷 / 03期

关键词：

D O I：

10.1007/BF01799402

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

[No abstract available]

引用

页码：387 / 389

页数：3

共 5 条

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POULOS, A ;

VANCRUGTEN, C ;

SHARP, P ;

CAREY, WF ;

ROBERTSON, E ;

BECROFT, DMO ;

SAUDUBRAY, JM ;

POLLTHE, BT ;

CHRISTENSEN, E ;

BRANDT, N .

EUROPEAN JOURNAL OF PEDIATRICS, 1986, 145 (06) :507-510

[2] ACCUMULATION OF PRISTANIC ACID (2, 6, 10, 14 TETRAMETHYLPENTADECANOIC ACID) IN THE PLASMA OF PATIENTS WITH GENERALIZED PEROXISOMAL DYSFUNCTION [J].

POULOS, A ;

SHARP, P ;

FELLENBERG, AJ ;

JOHNSON, DW .

EUROPEAN JOURNAL OF PEDIATRICS, 1988, 147 (02) :143-147

[3] DISTINCT LONG-CHAIN AND VERY LONG-CHAIN FATTY ACYL COA SYNTHETASES IN RAT-LIVER PEROXISOMES AND MICROSOMES [J].

SINGH, H ;

POULOS, A .

ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1988, 266 (02) :486-495

[4] A COMPARATIVE-STUDY OF STEARIC AND LIGNOCERIC ACID OXIDATION BY HUMAN-SKIN FIBROBLASTS [J].

SINGH, H ;

POULOS, A .

ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1986, 250 (01) :171-179

[5]

SINGH H, 1990, IN PRESS LIPID RES, V31

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