PEROXISOMAL 3-KETOACYL-COA THIOLASE IS PARTIALLY PROCESSED IN FIBROBLASTS FROM PATIENTS WITH RHIZOMELIC CHONDRODYSPLASIA PUNCTATA

被引：4

作者：

SUZUKI, Y ^{[1
]}

SHIMOZAWA, N ^{[1
]}

IZAI, K ^{[1
]}

UCHIDA, Y ^{[1
]}

MIURA, K ^{[1
]}

AKATSUKA, H ^{[1
]}

NAGAYA, M ^{[1
]}

YAMAGUCHI, S ^{[1
]}

ORII, T ^{[1
]}

机构：

[1] AICHI PREFECTURAL COLONY,KASUGAI 48003,JAPAN

来源：

JOURNAL OF INHERITED METABOLIC DISEASE | 1993年 / 16卷 / 05期

关键词：

D O I：

10.1007/BF00714280

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

[No abstract available]

引用

页码：868 / 871

页数：4

共 12 条

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[10] EFFECTS OF SODIUM 2-[5-(4-CHLOROPHENYL)PENTYL]OXIRANE-2-CARBOXYLATE (POCA) ON FATTY-ACID OXIDATION IN FIBROBLASTS FROM PATIENTS WITH PEROXISOMAL DISEASES
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