PANTETHINE DEPLETES CYSTINOTIC FIBROBLASTS OF CYSTINE

被引：14

作者：

BUTLER, JD ^{[1
]}

ZATZ, M ^{[1
]}

机构：

[1] NIMH, CELL BIOL LAB, BIOCHEM PHARMACOL UNIT, BETHESDA, MD 20205 USA

来源：

JOURNAL OF PEDIATRICS | 1983年 / 102卷 / 05期

关键词：

D O I：

10.1016/S0022-3476(83)80262-5

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

引用

页码：796 / 798

页数：3

共 14 条

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[2] ENZYMATIC BREAKDOWN OF PANTETHINE TO PANTOTHENIC ACID AND CYSTAMINE [J].

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[3]

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[4]

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[5]

LOWRY OH, 1951, J BIOL CHEM, V193, P265

[6] PANTETHEINASE ACTIVITY AND CYSTEAMINE CONTENT IN CYSTINOTIC AND NORMAL FIBROBLASTS AND LEUKOCYTES [J].

ORLOFF, S ;

BUTLER, JD ;

TOWNE, D ;

MUKHERJEE, AB ;

SCHULMAN, JD .

PEDIATRIC RESEARCH, 1981, 15 (07) :1063-1067

[7]

OSHIMA RG, 1974, J BIOL CHEM, V249, P6033

[8]

SCHNEIDER JA, 1978, METABOLIC BASIS INHE, P1660

[9]

SCHULMAN JD, 1972, DHEW NIH72249 PUBL

[10] TREATMENT OF GLUTATHIONE SYNTHETASE DEFICIENT FIBROBLASTS BY INHIBITION OF DELTA-GLUTAMYL TRANSPEPTIDASE WITH SERINE-BORATE [J].

SPIELBERG, SP ;

BUTLER, JDB ;

SCHULMAN, JD .

PEDIATRIC RESEARCH, 1978, 12 (04) :457-457

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