PERIPHERIN/RDS AND ROM-1 - MOLECULAR-PROPERTIES AND ROLE IN PHOTORECEPTOR CELL DEGENERATION

被引:42
作者
MOLDAY, RS
机构
[1] Department of Biochemistry and Molecular Biology, University of British Columbia, Vancouver
基金
英国医学研究理事会; 美国国家卫生研究院;
关键词
D O I
10.1016/1350-9462(94)90013-2
中图分类号
R77 [眼科学];
学科分类号
100212 ;
摘要
[No abstract available]
引用
收藏
页码:271 / 299
页数:29
相关论文
共 73 条
  • [1] AGARWAL N, 1991, RETINAL DEGENERATION, P489
  • [2] LOCALIZATION OF PERIPHERIN/RDS IN THE DISK MEMBRANES OF CONE AND ROD PHOTORECEPTORS - RELATIONSHIP TO DISK MEMBRANE MORPHOGENESIS AND RETINAL DEGENERATION
    ARIKAWA, K
    MOLDAY, LL
    MOLDAY, RS
    WILLIAMS, DS
    [J]. JOURNAL OF CELL BIOLOGY, 1992, 116 (03) : 659 - 667
  • [3] CLONING OF THE CDNA FOR A NOVEL PHOTORECEPTOR MEMBRANE-PROTEIN (ROM-1) IDENTIFIES A DISK RIM PROTEIN FAMILY IMPLICATED IN HUMAN RETINOPATHIES
    BASCOM, RA
    MANARA, S
    COLLINS, L
    MOLDAY, RS
    KALNINS, VI
    MCINNES, RR
    [J]. NEURON, 1992, 8 (06) : 1171 - 1184
  • [4] BASCOM RA, 1992, AM J HUM GENET, V51, P1028
  • [5] BASCOM RA, 1992, INVEST OPHTHALMOL S
  • [6] NUCLEOTIDE AND PREDICTED PROTEIN-SEQUENCE OF RAT RETINAL DEGENERATION SLOW (RDS)
    BEGY, C
    BRIDGES, CD
    [J]. NUCLEIC ACIDS RESEARCH, 1990, 18 (10) : 3058 - 3058
  • [7] MOLECULAR MECHANISM OF VISUAL TRANSDUCTION
    CHABRE, M
    DETERRE, P
    [J]. EUROPEAN JOURNAL OF BIOCHEMISTRY, 1989, 179 (02): : 255 - 266
  • [8] COHEN AI, 1983, INVEST OPHTH VIS SCI, V24, P832
  • [9] PHOTORECEPTOR PERIPHERIN IS THE NORMAL PRODUCT OF THE GENE RESPONSIBLE FOR RETINAL DEGENERATION IN THE RDS MOUSE
    CONNELL, G
    BASCOM, R
    MOLDAY, L
    REID, D
    MCINNES, RR
    MOLDAY, RS
    [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1991, 88 (03) : 723 - 726
  • [10] CONNELL G, 1991, RETINAL DEGENERATION, P467