SEVERE RECURRENT BACTERIAL-INFECTIONS ASSOCIATED WITH DEFECTIVE ADHERENCE AND CHEMOTAXIS IN 2 PATIENTS WITH NEUTROPHILS DEFICIENT IN A CELL-ASSOCIATED GLYCOPROTEIN

被引:207
作者
BOWEN, TJ
OCHS, HD
ALTMAN, LC
PRICE, TH
VANEPPS, DE
BRAUTIGAN, DL
ROSIN, RE
PERKINS, WD
BABIOR, BM
KLEBANOFF, SJ
WEDGWOOD, RJ
机构
[1] UNIV WASHINGTON, SCH MED, DEPT PEDIAT, SEATTLE, WA 98195 USA
[2] UNIV WASHINGTON, SCH MED, DEPT MED, SEATTLE, WA 98195 USA
[3] UNIV WASHINGTON, SCH MED, DEPT BIOCHEM, SEATTLE, WA 98195 USA
[4] PUGET SOUND BLOOD CTR, SEATTLE, WA 98104 USA
[5] TUFTS UNIV, NEW ENGLAND MED CTR, DEPT MED, BLOOD RES LAB, BOSTON, MA 02111 USA
[6] UNIV NEW MEXICO, DEPT MED & MICROBIOL, ALBUQUERQUE, NM 87131 USA
关键词
D O I
10.1016/S0022-3476(82)80013-9
中图分类号
R72 [儿科学];
学科分类号
100202 [儿科学];
摘要
引用
收藏
页码:932 / 940
页数:9
相关论文
共 42 条
[1]
RECURRENT INFECTIONS AND DELAYED SEPARATION OF THE UMBILICAL-CORD IN AN INFANT WITH ABNORMAL PHAGOCYTIC CELL LOCOMOTION AND OXIDATIVE RESPONSE DURING PARTICLE PHAGOCYTOSIS [J].
ABRAMSON, JS ;
MILLS, EL ;
SAWYER, MK ;
REGELMANN, WR ;
NELSON, JD ;
QUIE, PG .
JOURNAL OF PEDIATRICS, 1981, 99 (06) :887-894
[2]
DEFICIENCY OF A GRANULOCYTE-MEMBRANE GLYCOPROTEIN (GP150) IN A BOY WITH RECURRENT BACTERIAL-INFECTIONS [J].
ARNAOUT, MA ;
PITT, J ;
COHEN, HJ ;
MELAMED, J ;
ROSEN, FS ;
COLTEN, HR .
NEW ENGLAND JOURNAL OF MEDICINE, 1982, 306 (12) :693-699
[3]
BOWEN T, 1979, CLIN RES, V27, pA82
[4]
NEUTROPHIL ACTIN DYSFUNCTION AND ABNORMAL NEUTROPHIL BEHAVIOR [J].
BOXER, LA ;
HEDLEYWH.T ;
STOSSEL, TP .
NEW ENGLAND JOURNAL OF MEDICINE, 1974, 291 (21) :1093-1099
[5]
CORRECTION OF LEUKOCYTE FUNCTION IN CHEDIAK-HIGASHI-SYNDROME BY ASCORBATE [J].
BOXER, LA ;
WATANABE, AM ;
RISTER, M ;
BESCH, HR ;
ALLEN, J ;
BAEHNER, RL .
NEW ENGLAND JOURNAL OF MEDICINE, 1976, 295 (19) :1041-1045
[6]
BOYUM A, 1968, SCAND J CLIN LAB INV, VS 21, P77
[7]
AN INHERITED ABNORMALITY OF NEUTROPHIL ADHESION - ITS GENETIC TRANSMISSION AND ITS ASSOCIATION WITH A MISSING PROTEIN [J].
CROWLEY, CA ;
CURNUTTE, JT ;
ROSIN, RE ;
ANDRESCHWARTZ, J ;
GALLIN, JI ;
KLEMPNER, M ;
SNYDERMAN, R ;
SOUTHWICK, FS ;
STOSSEL, TP ;
BABIOR, BM .
NEW ENGLAND JOURNAL OF MEDICINE, 1980, 302 (21) :1163-1168
[8]
ALTERNATE-DAY PREDNISONE - LEUKOCYTE KINETICS AND SUSCEPTIBILITY TO INFECTIONS [J].
DALE, DC ;
FAUCI, AS ;
WOLFF, SM .
NEW ENGLAND JOURNAL OF MEDICINE, 1974, 291 (22) :1154-1158
[9]
MODULATING INFLUENCE OF CHEMOTACTIC FACTOR-INDUCED CELL ADHESIVENESS ON GRANULOCYTE FUNCTION [J].
FEHR, J ;
DAHINDEN, C .
JOURNAL OF CLINICAL INVESTIGATION, 1979, 64 (01) :8-16
[10]
FORLENZA SW, 1980, LANCET, V1, P567