BIOCHEMICAL STUDIES ON BRANCHED-CHAIN OXOACID OXIDASES

被引:19
作者
GOEDDE, HW
HUFNER, M
MOHLENBECK, F
BLUME, KG
机构
关键词
D O I
10.1016/0005-2744(67)90176-3
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:524 / +
页数:1
相关论文
共 11 条
[1]   METABOLISM OF THE WHITE BLOOD CELLS IN MAPLE-SYRUP-URINE DISEASE [J].
DANCIS, J ;
HUTZLER, J ;
LEVITZ, M .
BIOCHIMICA ET BIOPHYSICA ACTA, 1960, 43 (02) :342-343
[2]   THIN-LAYER CHROMATOGRAPHY AND SPECTROPHOTOMETRY OF ALPHA-KETOACID HYDRAZONES [J].
DANCIS, J ;
LEVITZ, M ;
HUTZLER, J .
BIOCHIMICA ET BIOPHYSICA ACTA, 1963, 78 (01) :85-&
[3]  
Goedde H W, 1966, Med Klin, V61, P2063
[4]   INVESTIGATIONS ON MAPLE SYRUP URINE DISEASE IN 2 FAMILIES [J].
GOEDDE, HW ;
RICHTER, E ;
HUFNER, M ;
VONZURMUHLEN, A .
HUMANGENETIK, 1964, 1 (02) :163-169
[5]   ARBEITSVORSCHRIFT EINES VEREINFACHTEN HETEROZYGOTENTESTES FUR DIE AHORNSIRUP-KRANKHEIT [J].
GOEDDE, HW ;
RICHTER, E ;
HUFNER, M ;
SIXEL, B .
KLINISCHE WOCHENSCHRIFT, 1964, 42 (16) :818-&
[6]   HETEROZYGOTENTEST FUR DIE AHORN-SIRUP-KRANKHEIT - BESTIMMUNG DER ENZYMAKTIVITAT DER ALPHA-KETOISOCAPRONSAUREOXYDASE IN LEUKOCYTEN [J].
GOEDDE, HW ;
SIXEL, B ;
STAHLMAN.C ;
RICHTER, E .
KLINISCHE WOCHENSCHRIFT, 1963, 41 (19) :953-&
[7]  
GOEDDE HW, BIOCHEMICAL GENETICS
[8]  
HOLT LE, 1960, FED PROC, V19, P10
[9]   MAPLE-SYRUP-URINE DISEASE - REPORT OF CASE WITH PEDIGREE [J].
LONSDALE, D ;
BARBER, DH .
NEW ENGLAND JOURNAL OF MEDICINE, 1964, 271 (26) :1338-&
[10]  
MENKES JH, 1954, PEDIATRICS, V14, P462