PORPHOBILINOGEN-SYNTHASE (DELTA-AMINOLEVULINIC-ACID DEHYDRATASE) DEFICIENCY IN BONE-MARROW CELLS OF 2 PATIENTS WITH PORPHOBILINOGEN-SYNTHASE DEFECT ACUTE PORPHYRIA

被引：7

作者：

DOSS, M ^{[1
]}

TIEPERMANN, RV ^{[1
]}

SCHNEIDER, J ^{[1
]}

机构：

[1] UNIV MARBURG, FAC MED, CLIN BIOCHEM & MED POLICLIN, D-3550 MARBURG, FED REP GER

来源：

KLINISCHE WOCHENSCHRIFT | 1983年 / 61卷 / 14期

关键词：

D O I：

10.1007/BF01487615

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

引用

页码：699 / 702

页数：4

共 20 条

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[8] ACUTE LEAD-POISONING IN INHERITED PORPHOBILINOGEN SYNTHASE (DELTA-AMINOLEVULINIC-ACID DEHYDRASE) DEFICIENCY [J].

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[9] NEW TYPE OF HEPATIC PORPHYRIA WITH PORPHOBILINOGEN SYNTHASE DEFECT AND INTERMITTENT ACUTE CLINICAL MANIFESTATION [J].

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[10] ACUTE HEPATIC PORPHYRIA SYNDROME WITH PORPHOBILINOGEN SYNTHASE DEFECT [J].

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SCHNEIDER, J .

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