SUCCESSFUL PREGNANCY IN A WOMAN WITH CONGENITAL FACTOR-XIII DEFICIENCY TREATED WITH SUBSTITUTIVE THERAPY - REPORT OF A 2ND CASE

被引:38
作者
RODEGHIERO, F [1 ]
CASTAMAN, GC [1 ]
DIBONA, E [1 ]
RUGGERI, M [1 ]
DINI, E [1 ]
机构
[1] SAN BORTOLO HOSP,CTR THROMBOSIS,I-36100 VICENZA,ITALY
来源
BLUT | 1987年 / 55卷 / 01期
关键词
D O I
10.1007/BF00319641
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:45 / 48
页数:4
相关论文
共 11 条
[1]   SUBUNITS A AND S INHERITANCE IN 4 FAMILIES WITH CONGENITAL FACTOR-XIII DEFICIENCY [J].
BARBUI, T ;
RODEGHIERO, F ;
DINI, E ;
MARIANI, G ;
PAPA, ML ;
DEBIASI, R ;
CORDEROMURILLO, R ;
MONTEROUMANA, C .
BRITISH JOURNAL OF HAEMATOLOGY, 1978, 38 (02) :267-271
[2]   HEREDITARY FACTOR-XIII DEFICIENCY - REPORT OF 4 FAMILIES AND DEFINITION OF THE CARRIER STATE [J].
BERLINER, S ;
LUSKY, A ;
ZIVELIN, A ;
MODAN, M ;
SELIGSOHN, U .
BRITISH JOURNAL OF HAEMATOLOGY, 1984, 56 (03) :495-505
[3]   GENETIC-HETEROGENEITY OF FACTOR-XIII DEFICIENCY - 1ST DESCRIPTION OF UNSTABLE A-SUBUNITS [J].
CASTLE, S ;
BOARD, PG ;
ANDERSON, RAM .
BRITISH JOURNAL OF HAEMATOLOGY, 1981, 48 (02) :337-342
[4]   DOCUMENTATION OF PLASMA FACTOR XIII DEFICIENCY IN MAN [J].
DUCKERT, F .
ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1972, 202 (DEC8) :190-199
[5]   FIBRIN STABILIZING FACTOR, FACTOR XIII [J].
DUCKERT, F .
BLUT, 1973, 26 (03) :177-179
[6]   FACTOR 13 DEFICIENCY WITH SEVERE HEMORRHAGIC DIATHESIS [J].
FISHER, S ;
RIKOVER, M ;
NAOR, S .
BLOOD-THE JOURNAL OF HEMATOLOGY, 1966, 28 (01) :34-&
[7]   TYPE-I AND TYPE-II DISEASE IN CONGENITAL FACTOR-XIII DEFICIENCY - A FURTHER DEMONSTRATION OF THE CORRECTNESS OF THE CLASSIFICATION [J].
GIROLAMI, A ;
CAPPELLATO, MG ;
LAZZARO, AR ;
BOSCARO, M .
BLUT, 1986, 53 (05) :411-413
[8]   DIAGNOSTIC AND GENETIC STUDIES ON FIBRIN-STABILIZING FACTOR WITH A NEW ASSAY BASED ON AMINE E INCORPORATION [J].
LORAND, L ;
URAYAMA, T ;
DEKIEWIE.JW ;
NOSSEL, HL .
JOURNAL OF CLINICAL INVESTIGATION, 1969, 48 (06) :1054-&
[9]  
Lorand L, 1980, Prog Hemost Thromb, V5, P245
[10]   FIBRIN CROSS-LINKING IN CONGENITAL FACTOR-XIII DEFICIENCY [J].
RODEGHIERO, F ;
BARBUI, T .
JOURNAL OF CLINICAL PATHOLOGY, 1980, 33 (05) :434-437