EHLERS-DANLOS SYNDROME - A VARIANT CHARACTERIZED BY THE DEFICIENCY OF PRO-ALPHA-2 CHAIN OF TYPE-I PROCOLLAGEN

被引:44
作者
SASAKI, T
ARAI, K
ONO, M
YAMAGUCHI, T
FURUTA, S
NAGAI, Y
机构
[1] TOKYO MED & DENT UNIV, MED RES INST, DEPT TISSUE PHYSIOL, CHIYODA KU, TOKYO 101, JAPAN
[2] MITSUI MEM HOSP, CTR CARDIOVASC DIS, TOKYO 101, JAPAN
关键词
D O I
10.1001/archderm.123.1.76
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
引用
收藏
页码:76 / 79
页数:4
相关论文
共 16 条
[1]   BIOCHEMICAL-COMPOSITION OF THE CONNECTIVE-TISSUE IN KELOIDS AND ANALYSIS OF COLLAGEN-METABOLISM IN KELOID FIBROBLAST-CULTURES [J].
ABERGEL, RP ;
PIZZURRO, D ;
MEEKER, CA ;
LASK, G ;
MATSUOKA, LY ;
MINOR, RR ;
CHU, ML ;
UITTO, J .
JOURNAL OF INVESTIGATIVE DERMATOLOGY, 1985, 84 (05) :384-390
[2]   FIBROBLASTS DEGRADE NEWLY SYNTHESIZED COLLAGEN WITHIN CELL BEFORE SECRETION [J].
BIENKOWSKI, RS ;
BAUM, BJ ;
CRYSTAL, RG .
NATURE, 1978, 276 (5686) :413-416
[3]   MARFAN-SYNDROME - ABNORMAL ALPHA-2 CHAIN IN TYPE-I COLLAGEN [J].
BYERS, PH ;
SIEGEL, RC ;
PETERSON, KE ;
ROWE, DW ;
HOLBROOK, KA ;
SMITH, LT ;
CHANG, YH ;
FU, JCC .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1981, 78 (12) :7745-7749
[4]   FLUOROGRAPHIC DETECTION OF RADIOACTIVITY IN POLYACRYLAMIDE GELS WITH THE WATER-SOLUBLE FLUOR, SODIUM-SALICYLATE [J].
CHAMBERLAIN, JP .
ANALYTICAL BIOCHEMISTRY, 1979, 98 (01) :132-135
[5]   MOLECULAR MECHANISMS HEPATIC-FIBROSIS .10. ACTIVATION OF COLLAGEN-SYNTHESIS IN PRIMARY CULTURE OF RAT-LIVER PARENCHYMAL-CELLS (HEPATOCYTES) [J].
HATA, RI ;
NINOMIYA, Y ;
SANO, J ;
KONOMI, H ;
HORI, H ;
SUNADA, H ;
TANAKA, S ;
KABUKI, K ;
NAGAI, Y ;
TSUKADA, Y .
JOURNAL OF CELLULAR PHYSIOLOGY, 1985, 122 (03) :333-342
[6]   BIOSYNTHESIS OF INTERSTITIAL TYPES OF COLLAGEN BY ALBUMIN-PRODUCING RAT-LIVER PARENCHYMAL-CELL (HEPATOCYTE) CLONES IN CULTURE .2. [J].
HATA, RI ;
NINOMIYA, Y ;
NAGAI, Y ;
TSUKADA, Y .
BIOCHEMISTRY, 1980, 19 (01) :169-176
[7]  
KISSANE JM, 1958, J BIOL CHEM, V233, P184
[8]  
KRANE SM, 1984, EXTRACELLULAR MATRIX, P413
[9]   QUANTITATIVE FILM DETECTION OF H-3 AND C-14 IN POLYACRYLAMIDE GELS BY FLUOROGRAPHY [J].
LASKEY, RA ;
MILLS, AD .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1975, 56 (02) :335-341
[10]   SPECTRUM OF CARDIAC DEFECTS IN THE EHLERS-DANLOS SYNDROME, TYPE-I AND TYPE-III [J].
LEIER, CV ;
CALL, TD ;
FULKERSON, PK ;
WOOLEY, CF .
ANNALS OF INTERNAL MEDICINE, 1980, 92 (02) :171-178